A novel case of polyfibromatosis and interstitial granulomatous dermatitis with arthritis

The granulomatous reaction pattern

“…736 Some patients present with arthralgias. 718,725,727,728,[743][744][745][746][747][748][749] Various infections have been associated with interstitial granulomatous dermatitis or a pattern similar to it. Other terms used include 'rheumatoid papules' and 'palisaded neutrophilic and granulomatous dermatitis'.…”

Interstitial granulomatous dermatitis: a distinct entity with characteristic histological and clinical pattern

“…In this study we report on cases encountered at our institution. Moreover, all the cases reported in the literature since 1993 were reviewed 4–36 . The results indicate that IGD is a distinct entity with a typical histological and clinical pattern, mostly presenting with papules and plaques on the trunk and proximal limbs.…”

Erosive Arthropathy with Osteolysis As a Typical Feature in Polyfibromatosis Syndrome: A Case Report and a Review of the Literature

“…Polyfibromatosis syndrome accompanied with erosive polyarthropathy is a rare dermatoarthropathy (1, 4, 5, 8) after the first historical description for polyfibromatosis syndrome by Tourain et al (3) in 1945. It seems that the presence of arthropathy in a patient with phenytoin-related polyfibromatosis was first described by Pierard et al (1) in 1979, although Black et al (4) used the term 'erosive arthropathy' in their description.…”

“…The biopsy results showed an increased number of osteoclasts associated with erosion of trabecular bone. Recently, a novel case of polyfibromatosis syndrome combined with interstitial granulomatous dermatitis and arthritis was also reported in the literature (8). Radiologic findings in a new form of an Australian case were also similar with the previous cases of polyfibromatosis syndrome.…”

“…Clinical and radiological characteristics for erosive arthropathy in polyfibromatosis have rarely been described, although comments about the presence of arthropathy in some cases have been presented in the literature (1, 4, 5, 8). Here, we described the radiological and clinical features for erosive arthropathy in our case and reviewed erosive arthropathy for cases with polyfibromatosis syndrome in previous reports.…”