A novel technique of abdominoplasty for prune belly syndrome

Abstract

Prune belly syndrome is an extremely rare congenital condition occurring predominantly in males. This triad syndrome comprises of partial or complete deficient abdominal wall muscles, undescended testes and dilated urinary collecting system. We present the case of a 2-year-old male patient, who presented with classic prune belly syndrome, operated with modification in classical Monfort technique of abdominoplasty. The basis of this approach was to save and use the supraumbilical abdominal wall which has better tensile strength. The infraumbilical skin was mostly discarded. The outcome was better in terms of cosmetic appearance as the scar was limited to the lower abdomen and better anterior abdominal wall strength.

The challenging diagnosis and management of the prune belly syndrome: A case report

“…Reconstruction surgical treatment may be necessary for all the congenital malformations mentioned above, such as urinary tract reconstruction, kidney transplantation, abdominoplasty, or orchidopexy. 9 , 13 The mortality rate is approximately 60%. The most frequent cause of death is kidney failure.…”