A Rare Association of Ebstein's Anomaly of Tricuspid Valve with Rheumatic Mitral Stenosis

Jayaprasad, N.; Thomas, Vinod; Shanmugavel, Madhavan; Rajesh, Gopalan Nair; Francis, Johnson; Venugopal, K

doi:10.1111/j.1540-8175.2007.00372.x

Cited by 4 publications

(5 citation statements)

References 3 publications

(3 reference statements)

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“…25 Dysplasia and restricted tricuspid leaflet motion can often be visualized. [28][29][30][31][32][33][34][35] Ebstein's anomaly is the most common cause of primary tricuspid regurgitation. The posterior 24 ) leaflet, which may be more severely involved than the septal leaflet, is best and most convincingly visualized in the right ventricular two-chamber view.…”

Section: Two-dimensional Echocardiographymentioning

confidence: 99%

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Echocardiographic Assessment of Ebstein's Anomaly

Booker

Nanda

2014

Echocardiography

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Ebstein's anomaly is a complex congenital lesion which primarily involves the tricuspid valve. The tricuspid leaflets are tethered to varying degrees to the right ventricular free wall and the ventricular septum often resulting in significant tricuspid regurgitation and a small functioning right ventricular chamber. Although the septal leaflet originates normally at the right atrioventricular junction, the proximal portion is often completely tethered to the ventricular septum resulting in a misconception and erroneous statements in many publications that its attachment is apically displaced. Although two-dimensional echocardiography represents the primary modality for the diagnosis of this anomaly, three-dimensional echocardiography provides incremental value in characterizing the extent and severity of tethering of individual tricuspid valve leaflets. This information is useful in surgical decision making whether to repair or replace the tricuspid valve.

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Section: Two-dimensional Echocardiographymentioning

confidence: 99%

“…26,27 Lastly, many other associated cardiac abnormalities can be positively identified with 2DTTE. [28][29][30][31][32][33][34][35] Ebstein's anomaly is the most common cause of primary tricuspid regurgitation. 26 As such, color Doppler is an essential component of the echocardiographic examination.…”

Section: Two-dimensional Echocardiographymentioning

confidence: 99%

Echocardiographic Assessment of Ebstein's Anomaly

Booker

Nanda

2014

Echocardiography

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“…In combination of Ebstein's with MS, atrial flutter or fibrillation with accelerated conduction via ACP may induce fast ventricular rate leading to precipitous increase in pulmonary venous pressure. therefore, tachyarrhythmia should be treated aggressively and ventricular rate should be controlled between 70 to 90 per minute [6]. preoperative electrophysiological evaluation is often warranted to locate aCp and possible rFa to avoid recurrent arrhythmia and instability in the perioperative period.…”

Section: Discussionmentioning

confidence: 99%

Perioperative Management for Surgical Repair of Ebstein's Anomaly.

Goga¹,

Kuçi²,

Ibrahimi³

et al. 2021

AJTES

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Background: Ebstein's anomaly is a rare and complex heart defect that affects the tricuspid valve and is accountable for around 1% of congenital cardiac abnormalities. It is one of the most common congenital causes of tricuspid valve regurgitation. Ebstein's anomaly often is diagnosed prenatally, due to its severe cardiomegaly. Some individuals with this anomaly do not experience complications until adulthood and even then, they have mostly minor complaints like exercise intolerance. An atrial septal defect is most commonly (70-90%) associated with Ebstein's anomaly. However, ventricular septal defect (VSD) can be associated with 2-6% of the cases. Case presentation: This report presents a case of surgical intervention for a 38-year-old female with Ebstein's anomaly symptomatic with moderate-severe pulmonary regurgitation and foramen ovale apertum. Conclusions: Ebstein anomaly is a complicated form of congenital heart disease with variable clinical presentations. The anesthetic plan must also focus on maintenance of RV function and avoidance of increase in PVR. Reversible causes of increased PVR, such as acidemia, hypoxemia, and hypercarbia must be avoided. Agents that lower PVR, such as nitrates, and nitric oxide may be beneficial in patients with severe pulmonary hypertension. With a sound knowledge of the cardiac anatomy, accurate scheming of surgical outcomes, routine follow-ups, multidisciplinary team approach, and better management, an experienced center can ultimately improve the prognosis of such patients.

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Section: Discussionmentioning

confidence: 99%

Anesthetic management for surgical repair of Ebstein′s anomaly along with coexistent Wolff-Parkinson-White syndrome in a patient with severe mitral stenosis

Sinha¹,

Kumar²,

Varma³

2010

Ann Card Anaesth

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Ebstein's anomaly (EA) is the most common cause of congenital tricuspid regurgitation. The associated anomalies commonly seen are atrial septal defect or patent foramen ovale and accessory conduction pathways. Its association with coexisting mitral stenosis (MS) has uncommonly been described. The hemodynamic consequences and anesthetic implications, of a combination of EA and rheumatic MS, have not so far been discussed in the literature. We report successful anesthetic management of a repair of EA and mitral valve replacement in a patient with coexisting Wolff-Parkinson-White (WPW) syndrome.

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A Rare Association of Ebstein's Anomaly of Tricuspid Valve with Rheumatic Mitral Stenosis

Cited by 4 publications

References 3 publications

Echocardiographic Assessment of Ebstein's Anomaly

Echocardiographic Assessment of Ebstein's Anomaly

Perioperative Management for Surgical Repair of Ebstein's Anomaly.

Anesthetic management for surgical repair of Ebstein′s anomaly along with coexistent Wolff-Parkinson-White syndrome in a patient with severe mitral stenosis

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