A Rare Case of Acroangiodermatitis Associated with a Congenital Arteriovenous Malformation (Stewart–Bluefarb Syndrome) in a Young Veteran: Case Report and Review of the Literature

Violaceous Plaques on the Left Lower Extremity

“…Biopsy reveals capillary proliferation in the dermis, extravasated red blood cells, tortuous vessels, and hemosiderin deposits. 4,5 Further staining with Verhoeff-van Gieson elastin and Perls iron stain can demonstrate thickened endothelial walls and hemosiderin deposition supporting abnormal vascular neoproliferation and shunting of blood, as seen in our patient; however, this step is not diagnostically necessary.…”

Acroangiodermatitis or pseudo-Kaposi’s sarcoma: a challenging diagnosis

“…Acroangiodermatitis is a dermatological condition characterized by purple-colored nodules, plaques or patches, mostly on the extensor surfaces of lower extremities [1]. There are four clinical variants of AAD, the most common type; Mali is associated with venous hypertension; the Stewart-Bluefarb type is associated with congenital arteriovenous malformation (AVM); there is also a less frequent one in patients with chronic renal failure with acquired arteriovenous fistula and a form occurring in pregnant women [3][4][5].…”

“…Acroangiodermatitis (AAD) is a rare angioproliferative disease usually of the lower limb manifesting with cutaneous lesions clinically similar to Kaposi's sarcoma [1]. It is a benign hyperplasia of preexisting vasculature and may be associated with acquired or congenital arteriovenous malformations (AVM), or severe chronic venous insufficiency [2][3]. The diagnosis relies mainly on histologic findings [4].…”