A rare case of pregnancy with Sturge-Weber syndrome

Pregnancy and refractory epilepsy in Sturge–Weber syndrome: Challenges and outcomes

“…Cesarean section was chosen electively without a provided reason to avoid theoretical risk of angioma rupture, or in cases of arrest of descent. The neurologic complications that arose did not seem to be directly related to the delivery 5–7,10–12,16 . Therefore, as SWS‐associated angiomas theoretically may be at risk of complications during the labor process, a more controlled delivery method, such as cesarean section, may be selected for a patient with large angiomas or a history of intracranial hemorrhage.…”

“…The neurologic complications that arose did not seem to be directly related to the delivery. [5][6][7][10][11][12]16 Therefore, as SWS-associated angiomas theoretically may be at risk of complications during the labor process, a more controlled delivery method, such as cesarean section, may be selected for a patient with large angiomas or a history of intracranial hemorrhage. Additionally, if general anesthesia is used, care should be taken to avoid agents that could increase intracranial pressure and thereby increase the risk of intracranial hemorrhage.…”

“…In several other cases, a more controlled delivery such as elective cesarean section, was chosen, at times citing the scarcity of information available on the safest mode of delivery. [10][11][12] One patient had a history of left-sided migraine associated with transient right hemiplegia and focal seizures consisting of paroxysmal spasm of the right limb since age 2, which were triggered by respiratory infections. At 17-weeks pregnant, these symptoms worsened in setting of a bacterial upper respiratory infection and severe vomiting.…”

Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

“…15 In case reports of SWS in pregnancy, the predominant mode of delivery (when the information is given) is by CS 9,10,17–19 often prompted by neurological deterioration or concerns, but influenced by maternal request in one case. 18 In one woman who had a small intraventricular haemorrhage four days post-delivery, labour had been induced, followed by a CS at full dilatation. 8 Another woman with SWS is reported to have two vaginal deliveries and uncomplicated epidurals, but she had a hemispherectomy performed as a child with no residual leptomeningeal angiomatosis (with non-contrast imaging).…”

“…Cardiac abnormalities are rare in SWS but septal defects, valvular lesions and transposition of the great vessels have been reported, and should be ruled out. 15 In case reports of SWS in pregnancy, the predominant mode of delivery (when the information is given) is by CS 9,10,17–19 often prompted by neurological deterioration or concerns, but influenced by maternal request in one case. 18 In one woman who had a small intraventricular haemorrhage four days post-delivery, labour had been induced, followed by a CS at full dilatation.…”