A rare isolated polycystic pancreatic disease. Radiation free diagnostic protocol in selected cases

Dhar, Dwivedi A N; Tripathi, Suchi; Garg, Sunny; Dixit, Vinod Kumar

doi:10.4103/2230-8210.103044

Cited by 5 publications

(5 citation statements)

References 4 publications

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“… 5 Other cases of concurrent feline PKD and DPMs have been reported, 6 – 8 and associated pancreatic cysts may also be present. 5 , 9 , 10 Autosomal dominant mutations in pkd1 have been discovered as the primary mutation associated with PKD in cats. 11 In this case, lack of appropriate sample collection for DNA testing precluded assessing for pkd1 mutation, and concurrent kidney cysts were not identified.…”

Section: Discussionmentioning

confidence: 99%

Severe polycystic liver disease in a cat

King,

Pappano,

Lorbach

et al. 2023

Journal of Feline Medicine and Surgery Open Reports

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Case summary Ductal plate malformations (DPMs) are poorly documented in the veterinary literature, particularly those of the polycystic liver disease (PCLD) phenotype. A 13-year-old female spayed cat presented with progressive icterus, abdominal distension, weight loss and elevated liver enzymes. Initial empirical treatment consisting of amoxicillin/clavulanate, ursodiol and later prednisolone was attempted; however, clinical signs progressed. On abdominal ultrasound, numerous large hepatic cystic masses were noted, characterized by an anechoic center with a heterogeneous, hyperechoic wall. A post-mortem examination confirmed numerous hepatic cysts, the larger of which resulted in hemorrhage and subsequent hemoabdomen. Histologically, these cysts were determined to be of biliary origin, and a diagnosis of PCLD was assigned. Relevance and novel information Herein, we present a detailed report of clinical, gross and histologic findings in a cat clinically affected by PCLD. This case demonstrates that cysts present in this congenital disease can ultimately lead to hepatobiliary malfunction and clinical decline via marked expansion of cysts, compression of the liver and hemoabdomen from cyst rupture. DPMs, specifically PCLD, should be considered in cats presenting with multifocal large hepatic cysts.

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Section: Discussionmentioning

confidence: 99%

Severe polycystic liver disease in a cat

King,

Pappano,

Lorbach

et al. 2023

Journal of Feline Medicine and Surgery Open Reports

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“…Congenital pancreatic cysts are largely asymptomatic, but can present with abdominal distension, vague abdominal pain, vomiting, jaundice, or pancreatitis. 5 - 7 Ultrasonography is particularly valuable for cystic/solid differentiation, and a color Doppler flow can demonstrate the vascular nature of lesions. 8 Cross-sectional imaging is eventually important in the characterization and localization of the cysts.…”

Section: Discussionmentioning

confidence: 99%

Polycystic Pancreas

Sonavane¹,

Amarapurkar²,

Amarapurkar³

2016

ACG Case Reports Journal

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“…Patients with PPD are usually asymptomatic, but can present with abdominal distention and abdominal pain. Rarely jaundice, vomiting or acute pancreatitis may present (3). Pancreatic cystic lesions are classified as neoplastic and non‐neoplastic cysts.…”

Section: Figurementioning

confidence: 99%

“…Isolated polycystic pancreas disease (PPD) is an extremely rare entity, with only a few reported cases (1–8). Patients with PPD are usually asymptomatic, but can present with abdominal distention and abdominal pain.…”

Section: Figurementioning

confidence: 99%

Polycystic Pancreas Disease

Ufuk

Tekinhatun²,

Alver³

2019

J. pediatr. gastroenterol. nutr.

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A 13-year-old girl with epigastric pain and abdominal distention was admitted to emergency room. Abdominal ultrasonography (US) revealed a multilocular giant cystic mass in the pancreas (Fig. 1). Abdominal magnetic resonance imaging (MRI) showed multiple cystic lesions in the pancreas. Septa, solid component, or contrast-enhancement was not detected in the cysts (Fig. 2). Normal pancreas parenchyma was only observed in the head and uncinate process. No pathological findings were found in other abdominal organs. Aspiration biopsy from the dominant cyst revealed fluid with pancreatic enzyme activity. Surgery for cyst evacuation was refused. Follow-up at 1 year with no treatment was uneventful.Isolated polycystic pancreas disease (PPD) is an extremely rare entity, with only a few reported cases (1-8). Patients with PPD are usually asymptomatic, but can present with abdominal distention and abdominal pain. Rarely jaundice, vomiting or acute pancreatitis may present (3). Pancreatic cystic lesions are classified as neoplastic and non-neoplastic cysts. Non-neoplastic pancreatic cysts are also described as retention cysts, congenital developmental cysts, enteric duplication cysts, abscesses, walled-off pancreatic necrosis, pseudocysts, and hydatid cysts. US and MRI can help differentiate malignant from benign pancreatic cysts. Multiple simple cysts, which diffusely involve pancreas on imaging studies suggest congenital-developmental cysts.

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A rare isolated polycystic pancreatic disease. Radiation free diagnostic protocol in selected cases

Cited by 5 publications

References 4 publications

Severe polycystic liver disease in a cat

Severe polycystic liver disease in a cat

Polycystic Pancreas

Polycystic Pancreas Disease

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