A Six Chambered Heart: Biventricular Outlet Obstruction in Association With Interventricular Septal Defect

Paredes, Santiago; Berger, Robert L.; Gardner, Thomas H.; Hipona, Florencio A.

doi:10.2214/ajr.111.4.771

Cited by 2 publications

(1 citation statement)

References 4 publications

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“…In our case, the six chambers of the heart were correctly diagnosed by preoperative echocardiography and CT-angiogram, facilitating the surgical planning beforehand. A six-chambered heart as described here was described around 50 years back but the morphology was entirely different [ 7 ].…”

Section: Discussionmentioning

confidence: 99%

A six-chambered heart: cor triatriatum sinister with double-chambered right ventricle in association with ventricular septal defect

et al. 2022

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Background Cor triatriatum has been described as a heart with three atria in which the left atrium (cor triatriatum sinistrum) or right atrium (cor triatriatum dextrum) is divided into two compartments by a fold of tissue, a membrane, or a fibromuscular band. Double-chambered right ventricle, on the other hand, is identified by the presence of an anomalous muscle bundle dividing the right ventricle into two chambers. Case presentation Here, we describe the case of a child who had a combination of both of these rare entities, effectively creating a heart with six chambers. The child underwent a successful intracardiac repair. Conclusions The association of CTS with DCRV forming a “6-chambered heart” is extremely rare. Awareness of its existence and accurate preoperative diagnosis has important implications in its surgical repair with all the components of this disease spectrum, further increasing the complexity of a successful surgical repair.

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Section: Discussionmentioning

confidence: 99%