Abdominal Lymphangiomatosis With Intestinal Lymphangiectasia Diagnosed by Magnetic Resonance Lymphangiography: A Case Report

A Patient with Retroperitoneal Cystic Lymphangiomatosis Confused with Serous Cystadenoma of the Pancreas

“…1 Retroperitoneal lymphatic malformations are very rare in this group and represent less than 1% of all abdominal lymphatic malformations. 11,12 It should be remembered that malformations that are adjacent to the pancreas as in our case may be confused with pancreatic cystic tumors due their cystic structural features. Contrast MRI or computed tomography (CT) and EUS sampling may be helpful in differential diagnosis.…”

“…13 Octreotide and tranexamic acid may be used in patients with moderate gastrointestinal bleeding. 11 In conclusion; lymphangiomatosis may present with diffuse organ involvement or may be large in size at a single site. Cases that were confused with metastatic disease due to diffuse bone involvement, hematologic malignancy due to spleen involvement and infectious causes (echinococcus, kala-azar etc.)…”

“…Lymphangioma is a congenital clinical phenomenon which can occur in any organ except brain that lacks lymphatics. 11 More than 90% of the patients are individuals below 2 years of age and it is often seen in the head and neck. 2 It is frequently asymptomatic in adulthood.…”

“…12 Patients who are not suitable for these and those who are refractory and symptomatic are candidates for surgery. 11 Intestinal lymphangiectasia usually respond to dietary changes such as a following low-fat diet and substitution of long-chain fatty acids with mid-chain fatty acids. 13 Octreotide and tranexamic acid may be used in patients with moderate gastrointestinal bleeding.…”

Lymphangiomatosis of the ileum with perforation: A case report and review of the literature

“…Lymphangiomatosis is a benign proliferation of lymph vessels. Lymphatic diseases can vary from small lymphangioma to generalized lymphangiomatosis, which is a rare condition and can have several clinical manifestations [ [1] , [2] , [3] , [4] , [5] , [6] ]. Although the underlying pathogenetic mechanism is unknown, it is generally considered as congenital malformation of the lymphatic system associated with alterations in the circulatory dynamics of the lymph [ 7 ].…”