Aberrant right subclavian artery: Varied presentations and management options

Stone, William M.; Brewster, David C.; Moncure, Ashby C.; Franklin, David P.; Cambria, Richard P.; Abbott, William M.

doi:10.1067/mva.1990.20386

Cited by 22 publications

(39 citation statements)

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“…5,6 However, some arch anomalies that do not produce vascular rings may ultimately have important clinical implications. 7 For instance, a left aortic arch and aberrant right subclavian artery can cause dysphagia because of esophageal compression later in life. 8 Moreover, a retroesophageal right subclavian artery may be prone to degenerative pathologic processes at the point where it passes between the esophagus and the vertebral column or to traumatic injury at its origin from the aorta.…”

Section: Discussionmentioning

confidence: 99%

Cardiovascular Anomalies in Patients Diagnosed With a Chromosome 22q11 Deletion Beyond 6 Months of Age

et al. 2001

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ABSTRACT. Objective. Cardiovascular anomalies are present in 75% to 80% of patients with a chromosome 22q11 deletion. In the majority of cases, the cardiovascular defect becomes evident in the neonatal period and is often the initial manifestation of the chromosome 22q11 deletion syndrome. However, a 22q11 deletion may also be associated with cardiovascular defects that are less obvious, such as a vascular ring, which may not be diagnosed until the patient is older. The objective of this study was to determine the frequency and types of cardiovascular anomalies in patients diagnosed with a chromosome 22q11 deletion beyond 6 months of age.Methods. We studied 29 patients diagnosed with a chromosome 22q11 deletion at a median age of 6.2 years (9 months to 45 years) who were subsequently referred for cardiovascular evaluation. Comprehensive cardiologic evaluation was performed, with transthoracic echocardiography (N ‫؍‬ 28) and/or magnetic resonance imaging (N ‫؍‬ 6), including imaging of the aortic arch. The frequency of cardiovascular anomalies diagnosed in these patients and the need for intervention were assessed.Results. Cardiovascular anomalies were detected in 11 (38%) patients: 3 with a vascular ring formed by a right aortic arch with an aberrant left subclavian artery and left-sided ligamentum arteriosum, 3 with a right aortic arch with mirror-image branching of the brachiocephalic arteries (no vascular ring; 1 with a patent ductus arteriosus), 4 with a left aortic arch with an aberrant right subclavian artery (no vascular ring; 1 with a patent ductus), and 1 with a left superior vena cava draining to the coronary sinus. The median age at diagnosis in these 11 patients was 3 years (9 months to 28 years). The remaining 18 patients had normal cardiovascular anatomy. All 3 patients with vascular rings subsequently underwent surgical repair, and 1 patient with a ductus arteriosus underwent transcatheter coil occlusion.Conclusions. The frequency of cardiovascular anomalies necessitating intervention in patients referred for cardiovascular evaluation after diagnosis of a chromosome 22q11 deletion beyond 6 months of age is 14% in our experience. Routine screening for cardiovascular anomalies, including echocardiography and other imaging studies to identify the laterality and branching pattern of the aortic arch, is indicated in patients diagnosed with 22q11 deletion beyond 6 months of age and is particularly critical for patients with respiratory or feeding disorders. Pediatrics 2001;108(6). URL: http://www. pediatrics.org/cgi/content/full/108/6/e104; velocardiofacial syndrome, DiGeorge syndrome, chromosome 22q11 deletion, vascular ring, aortic arch anomalies.

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Section: Discussionmentioning

confidence: 99%

Cardiovascular Anomalies in Patients Diagnosed With a Chromosome 22q11 Deletion Beyond 6 Months of Age

et al. 2001

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“…The variations described in literature are primarily of the right SA including its passage between the esophagus and the trachea (posterior to the esophagus) and its perforation or course anterior to the SAM (Stauffer and Pote, 1946;Sealy, 1951;Nathan and Seidel, 1983;Stone et al, 1990;Gabella, 1995). Only a few variations for the left SA have been described pertaining to its origin from the aortic arch (Gabella, 1995).…”

Section: Discussionmentioning

confidence: 97%

Cadaveric observation of an aberrant left subclavian artery: A possible cause of thoracic outlet syndrome

et al. 2005

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“…La arteria subclavia derecha aberrante de trayecto retroesofágico representa una variedad de anomalía del arco aórtico que puede ser incluida en la categoría de "anillo vascular" (Carrizo & Marjani, 2004), siendo detectada entre el 0,4 y el 2,0% de las autopsias (Stone et al, 1990), constituyendo la malformación más común del arco aórtico (Richardson et al, 1980). Si bien en la mayoría de los casos esta anomalía es asintomática, lo que explica su hallazgo incidental, el anillo vascular que encierra a la traquea y al esófago puede generar una compresión extrínseca de este último conducto, apareciendo el síntoma de disfagia (Fig.…”

Section: Discussionunclassified

Arteria Subclavia Aberrante

Inzunza

Burdiles

2010

Int. J. Morphol.

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RESUMEN:Se estudiaron las variaciones en el origen y trayecto de la arteria subclavia derecha aberrante, observada en un cadáver utilizado para docencia de anatomía humana. En este caso, el arco aórtico da origen a cuatro ramas separadas, que de derecha a izquierda son: arteria carótida común derecha, arteria carótida común izquierda, arteria subclavia izquierda y arteria subclavia derecha. Desde este origen, la arteria subclavia derecha transcurre por detrás de la tráquea y del esófago, a la altura del cuerpo vertebral de T III, para luego retomar su trayecto normal hacia la raíz del cuello. Se midieron los diámetros del arco aórtico y de sus ramas. Asimismo, se consignaron los díametros y la distancia de origen de ambas arterias vertebrales, desde las arterias subclavias. Esto se realizó con el objeto de analizar posibles asimetrías importantes relacionadas con la aparición de esta variación. En el texto se discuten las probables razones embriológicas que permiten explicar el origen anómalo de la arteria subclavia derecha.

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Aberrant right subclavian artery: Varied presentations and management options

Cited by 22 publications

References 0 publications

Cardiovascular Anomalies in Patients Diagnosed With a Chromosome 22q11 Deletion Beyond 6 Months of Age

Cardiovascular Anomalies in Patients Diagnosed With a Chromosome 22q11 Deletion Beyond 6 Months of Age

Cadaveric observation of an aberrant left subclavian artery: A possible cause of thoracic outlet syndrome

Arteria Subclavia Aberrante

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