Achenbachs syndrome revisited

Thies, Katharina; Beschorner, Ulrich; Noory, Elias; Zeller, Thomas

doi:10.1024/0301-1526/a000223

Cited by 21 publications

(24 citation statements)

References 0 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Another explanation of the reduced blood flow might be compression by the hematoma [4]. In contrast to these dynamic causes of hypoperfusion, hypoplasia of the ulnar artery on the same hand side has also been described [10]. In our patient also lower arm arteries were rather small, and blood flow was reduced even outside of an attack.…”

Section: Case Reportmentioning

confidence: 52%

“…Achenbach's syndrome occurs more frequently in women than in men [5,9,10]. Affected patients are younger than those who suffer from peripheral vascular disease, but the onset might be later than that of Raynaud's syndrome [1].…”

Section: Discussionmentioning

confidence: 99%

“…Kordzadeh, et al included 12 cases into their re- [2]. In the meantime, patients are typically asymptomatic besides residual venectasia on the volar side of the hand and fingers, especially in the regions of the joints [2,10]. This is thought to be the origin of the typical hematoma [4].…”

Section: Discussionmentioning

confidence: 99%

“…The symptoms had first occurred on the right side af-view of Achenbach's syndrome in 2015 [9], but missed out on the cases by Achenbach himself, Jung, Singer and Nitzschner [2,[4][5][6] in the German-speaking literature of the 1950s and 1960s, as well as on a more recent case series from Germany by Thies, et al [10]; with Jung [4] presenting a series of as many as 40 cases, they sum up to another 65 cases. Interestingly, there have been a few more case reports on Achenbach's syndrome in the international literature just lately, all of which are from Japan [11][12][13].…”

Section: Case Reportmentioning

confidence: 99%

See 3 more Smart Citations

Painful Hand Swelling after a Roller Coaster Ride

Felicitas¹,

Britta²,

Boris³

et al. 2018

Clin Med Rev Case Rep

View full text Add to dashboard Cite

We present a case report on the Achenbach's syndrome, a condition characterized by a painful hematoma and swelling of the palmar side of the hand and/or fingers with a sudden onset. Symptoms are typically triggered by everyday activities like carrying a bag or pressing down a door handle. Achenbach's syndrome being rather unknown, its impressive clinical presentation might unsettle both patients and physicians and entail elaborate diagnostic measures despite its in fact benign and self-limiting character.ter performing manual labour about ten months ago; thereafter, the patient preferably used the left hand, where the same symptoms occurred. Another time, the symptoms had once been provoked by a roller-coaster ride. The symptoms were self-limiting after two weeks at the most. When the patient presented himself to our department, there was no discoloration visible, however he described residual tightness in the fingers of both hands, which was improvable by cooling. The patient reported to avoid manual labour and exposure to heat in fear of provoking the symptoms again. Smoking was stopped more than ten years ago, and there were no comorbidities obviously related to the symptoms. The patient did not take any medication and had not received any treatment for his symptoms.Before the presentation to our department, a series of MR-angiography scans had already been performed. These had shown circular angiomatous alterations along the phalanges, less along the metacarpalia of D II -IV on both hands (Figure 1). The patient was then referred to our department for further evaluation of the suspected angiomatous malformation. On physical examination, the veins in the palms of both hands appeared to prominently shine through the skin; there was no swelling or neurological dysfunction. Duplex ultrasound of the arm arteries revealed a normal triphasic pattern with rather slow flows in the lower arm of 39 cm/sec in the ulnar artery and of 32 cm/sec in the radial artery; ultrasound of the carotid arteries and the aorta did not show any abnormalities. On the oscillography of the finger arteries, the amplitudes were slightly re-

show abstract

Section: Case Reportmentioning

confidence: 52%

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Section: Case Reportmentioning

confidence: 99%

See 2 more Smart Citations

Painful Hand Swelling after a Roller Coaster Ride

Felicitas¹,

Britta²,

Boris³

et al. 2018

Clin Med Rev Case Rep

View full text Add to dashboard Cite

show abstract

“…Singer [19] favoured the hypothesis of a vasomotor disorder, and the association of PFH with Raynaud phenomenon was recently brought into focus by Thies et al [21] who found three patients with Raynaud in a series of eight women with PFH. This is consistent with the epidemiological associations we found, both with Raynaud phenomenon and with a history of chilblains.…”

Section: Discussionmentioning

confidence: 99%

Paroxysmal finger haematoma - a benign acrosyndrome occurring in middle-aged women

Carpentier

Maricq

Biro

et al. 2016

Vasa

View full text Add to dashboard Cite

Summary:Background: Paroxysmal fi nger haematoma (PFH) is an under-recognised vascular acrosyndrome with no epidemiological description to date. The aim of this work was to evaluate the prevalence, risk factors and clinical correlates of PFH in a population-based sample of subjects and to describe their semiological characteristics. Patients and methods: This cross-sectional study of random samples of the general population in three geographic areas of France involved 802 subjects, 548 women and 254 men, aged 18 to 84 years. The diagnosis of PFH was made from a report by the subject of a history of recurrent haematoma in the fi ngers with a sudden, painful and unexpected occurrence. Diagnosis of associated conditions and evaluation of lifestyle variables were obtained through standardised medical interview and examination. Results: A history of PFH was detected in 71 subjects, with a prevalence of 1.2 % in men and 12.4 % in women; there was no signifi cant regional variation. Onset before 40 years of age was rare. Besides female sex and age, no socio-economical nor lifestyle risk factors were detected. PFH was associated with Raynaud phenomenon and a history of chilblains, but no link with any health threatening disease was found. In addition to the sudden onset of pain and hematoma, the main clinical features were a frequent digital swelling during the painful attack, and their predominant location on the volar side of the fi rst and second phalanges of the third or second fi ngers of the dominant hand. Conclusions: PFH is a benign phenomenon, frequently found in middle-aged women, to be classifi ed among the vascular acrosyndromes. Patients seeking medical evaluation for this disorder should be reassured.

show abstract

Acquired Disorders of Dermal Connective Tissue

Lovell

2016

Rook's Textbook of Dermatology, Ninth Edition

View full text Add to dashboard Cite

The subject matter of this chapter comprises the major acquired disorders that affect mainly collagen and elastic tissue. The connective tissue of normal skin is discussed elsewhere. Heritable disorders of connective tissue, such as Ehlers–Danlos syndrome, are covered in another chapter, as are disorders of ground substance, such as the mucinoses and mucopolysaccharidoses. In addition, many disorders, including developmental defects, neoplasms and other reactive or scarring conditions, may involve the connective tissues. Although it can be convenient to separate conditions into disorders affecting collagen or elastic tissue, the distinction is somewhat artificial, as changes in these proteins are generally preceded by abnormal metabolism of other matrix components, such as fibronectin or periostin.

show abstract

Achenbachs syndrome revisited

Abstract: We stress the need for greater awareness among clinicians of the harmlessness of the condition in order to avoid misdiagnoses and dispensable diagnostic procedures.

Cited by 21 publications

References 0 publications

Painful Hand Swelling after a Roller Coaster Ride

Painful Hand Swelling after a Roller Coaster Ride

Paroxysmal finger haematoma - a benign acrosyndrome occurring in middle-aged women

Acquired Disorders of Dermal Connective Tissue

Contact Info

Product

Resources

About

Achenbachs syndrome revisited

Abstract: We stress the need for greater awareness among clinicians of the harmlessness of the condition in order to avoid misdiagnoses and dispensable diagnostic procedures.

Cited by 21 publications

References 0 publications

Painful Hand Swelling after a Roller Coaster Ride

Painful Hand Swelling after a Roller Coaster Ride

Paroxysmal finger haematoma - a benign acrosyndrome occurring in middle-aged women

Acquired Disorders of Dermal Connective Tissue

Contact Info

Product

Resources

About

Achenbachs syndrome revisited