Acquired Brown's syndrome in a patient with combined lichen sclerosus et atrophicus and morphoea.

Ophthalmic findings in linear scleroderma manifesting as facial en coup de sabre

“…Occasional case reports on ECS have presented data on external eye muscles (diplopia) and/or inflammatory changes (episcleritis, uveitis) [4][5][6][7][8][9][10]. Central nervous system involvement has also been discussed [11][12][13][14].…”

Bilateral Acquired Brown Syndrome in Systemic Scleroderma

“…It can be localized to the skin (coup de sabre) or generalized with visceral organ involvement (systemic sclerosis). Acquired Brown syndrome associated with the localized form of scleroderma (combined lichen sclerosus et atrophicus and morphea) has been previously reported, 5 and orbital involvement is known as one of the rare complications of localized scleroderma. 7 Thus, restrictive ophthalmopathy was previously known as associated with only localized forms of scleroderma, in which maximal involvement is observed on the areas immediately subjacent to the area of linear scleroderma.…”

“…Nontraumatic inflammatory causes of acquired Brown syndrome have been reported to include rheumatoid arthritis, 3 juvenile chronic arthritis, 4 and localized scleroderma. 5 Traumatic causes are either surgical or more commonly nonsurgical, when a sharp instrument enters the upper nasal quadrant of the orbit. Occasionally, a patient appears to develop Brown syndrome without obvious cause.…”

Linear scleroderma with orbital involvement: follow up and magnetic resonance imaging

“…Olver et al have reported a patient with bilateral acquired Brown’s syndrome and combined lichen sclerosus et atrophicus and morphoea 4. They suggest that the deep subdermal fibrosis may limit the passive movement of the superior oblique tendon.…”