Acquired cutis laxa following urticarial vasculitis associated with IgA myeloma

Turner, Ryan B.; Haynes, Harley A.; Granter, Scott R.; Miller, Danielle M.

doi:10.1016/j.jaad.2008.09.059

Cited by 21 publications

(18 citation statements)

References 36 publications

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“…[101][102][103][104][105][106][107][108][109][110][111][112][113][114][115][116][117][118] ACL often starts on the face and progresses caudally. 105 Some patients have systemic involvement with emphysema, intestinal diverticula, hernias, and vascular dilatations.…”

Section: Acquired CLmentioning

confidence: 99%

“…105, 119 Marshall syndrome is a type of ACL affecting young children and characterized by postinflammatory elastolysis after a neutrophilic dermatosis (Fig 7, B). 113,114,117 Patients with ACL may demonstrate low lysyl oxidase activity, high cathepsin G levels, and reduced alpha-1-antitrypsin, presumably contributing to decreased cutaneous elastin. 120 One patient with ACL demonstrated missense mutations in ELN and FBLN5, suggesting that mild mutations in CL genes may increase susceptibility to inflammatory destruction of elastic fibers.…”

Section: Acquired CLmentioning

confidence: 99%

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Cutis laxa: A review

Berk

Bentley

Bayliss

et al. 2012

Journal of the American Academy of Dermatology

182

155

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Section: Acquired CLmentioning

confidence: 99%

Section: Acquired CLmentioning

confidence: 99%

Cutis laxa: A review

Berk

Bentley

Bayliss

et al. 2012

Journal of the American Academy of Dermatology

182

155

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“…Cutis laxa is a rare congenital or acquired connective tissue disorder manifested as loose and redundant skin folds due to abnormal skin elasticity . The inherited form of cutis laxa is uncommon and frequently autosomal recessive, but it can also be inherited as autosomal dominant or X‐linked .…”

Section: Discussionmentioning

confidence: 99%

Bilateral Congenital Entropion with Cutis Laxa

Al-Faky

Salih

Mubarak

et al. 2014

Pediatric Dermatology

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Cutis laxa is a rare connective tissue disorder characterized by redundant and pendulous skin due to a defect in the elastic fiber network. Two cases of entropion associated with cutis laxa have been reported, although entropion was due to elongation of the anterior lamella or horizontal lid laxity. Thorough systemic and ophthalmic evaluations were performed, as well as chart review for the perinatal period. Surgical correction of entropion through posterior tarsotomy was done. An infant boy with dysmorphic features and furrowing of the skin of the entire body without hyperelasticity, which is typical for cutis laxa, presented with bilateral congenital entropion. We report here for the first time a different etiology of congenital entropion with cutis laxa: the eyelashes were abnormally directed due to the unusual location of their roots, which were embedded within the tarsus. Moreover, this is the only case of cutis laxa with congenital entropion involving both upper and lower eyelids. Congenital entropion can be associated with cutis laxa. Although elongation of the anterior lamella and horizontal lid laxity predispose to such an entropion, abnormal location of the roots of the eyelashes might be encountered and marginal eyelid rotation surgery is indicated.

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“…There are other rare associated cutaneous findings in UV patients reported in the literature. A case with rapidly progressing acquired cutis laxa following involvement of the skin areas with lesions of NUV was reported [92]. A reported pregnant woman developed acquired reactive perforating collagenosis at the sites of resolved UV lesions 3 weeks following the onset and treatment of UV [19].…”

Section: Course and Prognosismentioning

confidence: 99%

Urticarial Vasculitis

Koç¹,

Aksoy²,

Tatlıparmak³

2017

A Comprehensive Review of Urticaria and Angioedema

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Urticarial vasculitis (UV) is a small vessel vasculitis and an immune-complex mediated disease like other leukocytoclastic vasculitis. UV seems similar to common urticaria clinically. Major difference between urticarial vasculitis and urticaria is the duration of lesions. Urticarial lesions regress in 24 hours, but UV lesions persist longer than 24 hours. Residual hyperpigmentation, constitutional symptoms like fever, arthralgia, and abdominal pain are other main clinical differences between these disorders. Upon confirmation of diagnosis, patients are divided into two major categories on the basis of serum complement levels: normocomplementemic UV (NUV) and hypocomplementemic UV (HUV). Consensus meeting in 1996 stated that long lasting (at least 24 hour-5 days) indurated wheals, which may be itchy, painful or tender, be associated with purpura and presence of associated extracutaneous findings, and cutaneous vasculitis confirmed by histopathological examination are defined as UV.

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Acquired cutis laxa following urticarial vasculitis associated with IgA myeloma

Cited by 21 publications

References 36 publications

Cutis laxa: A review

Cutis laxa: A review

Bilateral Congenital Entropion with Cutis Laxa

Urticarial Vasculitis

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