Acquired nonsurgical complete atrioventricular block in a child with endocardial cushion defect

Mehta, Ashok V.; O'Riordan, Anna C.; Sánchez, Guillermo R.; Black, Iain

doi:10.1002/clc.4960051106

Cited by 12 publications

(8 citation statements)

References 7 publications

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“…We report on 2 cases -the first was a male child known to have had a proionged P-R interval ; the second was an I I year-old girl, who , 2 years before surgery, developed comp lete atrioventricular biock subsequen t Dr Received fo r pub lication: Jul y 7,1985 to first degree atrioventricular block . The clinical findings in the latter case have been reported previously (6).…”

supporting

confidence: 62%

“…Furthermore, it has been reported that adults with atrioventricular sep tal defects can develop a progre ssive lengthening of the P-R inte rval which can lead to complete atrioventricular block (1 1, 13). Alth ough progre ssive heart block has been observed in adolescents with congenitally corre cted transposition (5 , 8) it is less well recognized in children with atrioventricular septal defect (6). Histological studi es on the cardiac conduction system of children with atriov entricular septal defect and atri oventricular conduction distu rbances recorded befo re submission to surgical repair are scarce.…”

mentioning

confidence: 99%

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Heart Block and Atrioventricular Septal Defect

Ho¹,

Rossi²,

Mehta³

et al. 1985

Thorac cardiovasc Surg

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The cardiac conduction system was examined in 2 hearts which had repair of atrioventricular septal defect. The first was from a child known to have had a prolonged P-R interval and the second was from a girl who developed complete heart block before submission to surgery. The atrioventricular conduction axis was histologically discontinuous in the first case, but preserved and surrounded by hemorrhage in the second case. This study draws attention to the inherent vulnerability of the cardiac conduction axis which must also be recognized before surgical intervention.

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supporting

confidence: 62%

mentioning

confidence: 99%

Heart Block and Atrioventricular Septal Defect

Ho¹,

Rossi²,

Mehta³

et al. 1985

Thorac cardiovasc Surg

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“…Both sinus node and AV nodal conduction abnormalities have been reported in patients with ASDs. Electrophysiologic markers of sinus node dysfunction have been described in many patients with ASDs (9,21). Clinical sinus node dysfunction has been reported both pre-and postprocedurally for ostium secundum ASDs and ostium primum ASDs (9).…”

Section: Conduction Disordersmentioning

confidence: 99%

Arrhythmias and conduction disorders associated with atrial septal defects

Williams¹,

Perry²

2018

J. Thorac. Dis.

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Atrial septal defects (ASDs) are the most common form of congenital heart disease. There are 4 embryologic types of ASDs, and rhythm considerations vary based on type. ASDs have left-to-right shunt and primarily right-sided volume overload. This leads to electrical remodeling that may predispose patients to atrial tachyarrhythmias and conduction disorders. Risk for arrhythmias is increased with late age of ASD repair, shunt size, other factors such as pulmonary hypertension and comorbid conditions. Arrhythmia incidence is decreased after ASD closure, but remains elevated compared to general population. Medical and procedural therapy for arrhythmias should consider type and timing of ASD repair. Conduction disorders are rare. Sinus node dysfunction may be seen with late age of repair and large shunt size. Sinus venosus ASD exhibits a higher rate of sinus node dysfunction, especially with older surgical techniques. Ostium primum ASD has higher risk of spontaneous or post-operative AV block, though this is rare with current surgical techniques. Risk of AV block with surgical repair or device closure of secundum ASD is rare. Familial ASDs and other forms of congenital heart disease may be seen with mutations in associated myocardial transcription factors NKX2.5, GATA4, TBX6, along with conduction disorders such as AV block.

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“…Lesions particularly associated with inherent abnormalities of the conduction system include atrioventricular septal defects with common atrioventricular junction, visceral heterotaxy in the setting of isomeric atrial appendages, and lesions with discordant atrioventricular connections, as typically seen in congenitally corrected transposition. 1,2 Individuals with these lesions should be frequently evaluated for progression of disease afflicting the conduction system, even if they appear to have normal atrioventricular conduction at birth. The conduction system is thought to be vulnerable due to anatomic factors, such as the anterior and superior displacement of the atrioventricular node leading to a longer course of the bundle of His.…”

Section: Pacing For Bradycardiamentioning

confidence: 99%

Current state of the art for use of pacemakers and defibrillators in patients with congenital cardiac malformations

Stephenson

Kaltman

2006

Cardiol Young

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As patients with congenital cardiac malformations increasingly survive therapeutic interventions, and our understanding of primary electrical diseases increases, the landscape of paediatric and congenital electrophysiology is expanding. Electrophysiologic abnormalities, both tachycardic and bradycardic, are commonly seen in post-operative patients with congenital cardiac disease, as well as being part of the natural history of congenital malformations and cardiomyopathies. Disturbances of rhythm represent an increasing morbidity in this population, and therapies using devices in the form of pacemakers and implantable cardioverter-defibrillators have taken on a correspondingly important role. In this review, we discuss some of the key features and recent advances in pacing for bradycardia, resynchronization pacing, anti-tachycardia pacing, and use of implantable cardioverter-defibrillators.

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Acquired nonsurgical complete atrioventricular block in a child with endocardial cushion defect

Cited by 12 publications

References 7 publications

Heart Block and Atrioventricular Septal Defect

Heart Block and Atrioventricular Septal Defect

Arrhythmias and conduction disorders associated with atrial septal defects

Current state of the art for use of pacemakers and defibrillators in patients with congenital cardiac malformations

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