Acrosyringeal variant of extragenital lichen sclerosus et atrophicus

Abstract

Lichen sclerosus et atrophicus (LSA) is a chronic inflammatory dermatosis of the anogenital area, and approximately 15% to 20% of patients with LSA have extragenital lesions. Here, we report the case of an 18-year-old Korean man presenting with multiple asymptomatic punctated hypopigmented atrophic macules on the dorsa of both feet. Dermoscopic examination revealed hypopigmented atrophic macules with several central keratotic plugs. The histopathologic findings indicated LSA but were confined to the acrosyringium. Based on the clinical and histopathological findings, the patient was diagnosed with an acrosyringeal variant of extragenital LSA. The patient in this case showed a unique histopathological finding in which the typical features of LSA were confined to the acrosyringium, as well as an unusual clinical presentation of non-coalescing atrophic punctate macules on the dorsum of the feet.

Adnexotropic Variants of the Interface Dermatitides: A Review

“…A syringotropic variant has also been described in a patient with hypopigmented atrophic macules on the dorsa of his feet. Histopathology revealed classical pathologic findings of LSA in addition to eccrine duct dilation, lymphocytic inflammation around the eccrine glands, and a band-like lymphocytic infiltrate around the acrosyringium [25].…”