Actions of nursing care in the infant with west syndrome: a case report

Abstract

Objective: To systematize nursing care to an infant with West Syndrome, using the Nomenclature of Diagnoses / Results and Nursing Interventions. Methods: Descriptive study, a case study, conducted at a School Hospital in João Pessoa / Paraíba in October 2010, following the phases of the nursing process. Diagnoses were identified using the Nomenclature of Diagnoses / Results and Nursing Interventions developed and validated for said hospital according to CIPE® terms. The project was approved by the Research Ethics Committee of the hospital under CAAE: 0052.0.126.000-09. Results: Six nursing diagnoses were identified: neuropsychomotor impairment, seizure, impaired oral hygiene, altered respiratory pattern, risk of infection, altered family routine. Conclusion: The use of a nomenclature of diagnoses / results and interventions directs the actions of nursing, providing efficiency in the care of children with West syndrome

West Syndrome – Infantile Spasms: A Rare Paediatric Case Report

“…Even if part of the symptoms is absent, WS is defined by a triad of symptoms, including epileptic spasms, stop or regression of psychomotor development, and hypsarrhythmia on interictal electroencephalography (EEG). 2,3 William West, an English doctor, first characterized the disease in 1841. Dr. Gastaut, Poirier, and Pampiglione coined the term "West Syndrome" in the early 1960s.…”

West Syndrome: Report of Clinical Case: 9 Years of Follow-up

“…WS is a rare and severe childhood epilepsy syndrome. Even if some of the symptoms are missing, WS is defined by a triad of them, including epileptic spasms, arrest or regression of psychomotor development, and hypsarrhythmia on interictal electroencephalography (EEG) [2,3]. WS was one of the first epilepsy syndromes described.…”

“…The incidence of WS is 1 per 2000-4000 individuals born alive. It is more frequent in males; it is responsible for 2-10% of the causes of childhood epilepsies [2] and can be associated with other systemic conditions or syndromes [6]. WS occurs in children from all ethnic groups [3].…”

“…Some epileptic syndromes, such as WS, can evolve catastrophically by a major impact on the cognitive and neuromotor development of the patients due to the difficulty in controlling the crisis and the association with intellectual disabilities [1]. The presence of mental retardation is observed in 90% of the cases, half of the patients with severe mental disabilities; psychiatric disorders are common; 50-60% of the cases developed into Lennox-Gastaut syndrome; multifocal epilepsy; or secondarily generalized partial epilepsy [2].…”

“…There are two drugs with evidence of efficacy in the treatment of WS: ACTH hormone and the Vigabatrin [1,7]. Pyridoxine, Valproic Acid, Lamotrigine, Topiramate, Prednisone, Phenobarbital [7], Carbamazepine, or Phenytoin [1,2] are also used.…”