Acute Soft Skull Syndrome in an Adult Male with Sickle Cell Anemia in Sudan: A Case Report

Taha, Ziryab Imad; Mohammed, Sulafa Eisa; Essa, Mohammed Elmujtba Adam; Elsid, Walaa Mohamed; Hussein, Mustafa Mohamed Ali; Osman, Sherihan Mohammed Elkundi; Ahmed, Hussein Osman; Yousif, Mutwaly Defealla; Ahmed, Abdelkareem A.

doi:10.14218/erhm.2019.00024

Cited by 2 publications

(2 citation statements)

References 17 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Lack of advanced brain imaging services in SSA is major hurdle in managing patients where ICH is of potential concern. However, in the absence of ICH, complete resolution of ASHS is the rule, on conservative management 30,33,37 . Thus, a high index of suspicion for ASHS is critical, particularly where advanced diagnostic services are not readily available.…”

Section: Discussionmentioning

confidence: 99%

“…However, in the absence of ICH, complete resolution of ASHS is the rule, on conservative management. 30 , 33 , 37 Thus, a high index of suspicion for ASHS is critical, particularly where advanced diagnostic services are not readily available. Nevertheless, patients with initial episode of ASHS are at increased risk of recurrency and ICH, thus, patients would still require long‐term follow up.…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

Acute soft head syndrome in a teenager with sickle cell anemia: A case report

Magitta,

Komanya,

Alphonce

et al. 2023

Clinical Case Reports

View full text Add to dashboard Cite

Key Clinical MessageSickle cell disease (SCD) rarely presents with acute soft head syndrome (ASHS) often posing a diagnostic dilemma. Recovery is typically spontaneous, however, in the context of lack of awareness and limited brain imaging it could potentially lead to poor outcome.AbstractASHS is a rare complication of SCD, invariably occurring near puberty with hitherto elusive pathogenic mechanisms. ASHS often resolves spontaneously on conservative management, however, lack of awareness in the context of limited access to brain imaging could pose diagnostic challenges resulting in inappropriate management and untoward outcome. We present a case of a teenager who presented with subtle symptoms for which the diagnosis of sickle cell anemia (SCA) was delayed until he developed ASHS. LTM was a 16 years old boy with a history of recurrent joints pain since the age of 6 years, with a family history of SCA, but had initial negative sickling test. He presented with episodes of multiple joints pain, unprovoked scalp and left orbital swelling, low‐grade fever and mild headache without any evidence for bleeding diathesis. The diagnosis of SCA was confirmed by hemoglobin electrophoresis. Computed tomography (CT) scan of the head revealed subgaleal heamatoma (SGH) and intraorbital haematoma without intracranial hemorrhage (ICH). He was managed conservatively with analgesics and hydration together with antibiotics for associated sepsis with complete resolution of clinical symptoms within 2 weeks. This case represents a rare scenario for a relatively mild SCA phenotype presenting with ASHS whose diagnosis poses an enigma in the resource‐limited contex. It is therefore, prudent to recognize ASHS to avoid judicious interventions which could potentially result in untoward clinical outcome.

show abstract

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Acute soft head syndrome in a teenager with sickle cell anemia: A case report

Magitta,

Komanya,

Alphonce

et al. 2023

Clinical Case Reports

View full text Add to dashboard Cite

show abstract

Unilateral Facial Swelling in a Sickle Cell Patient

Akhouri,

Fowler,

Schwarz

et al. 2024

Cureus

View full text Add to dashboard Cite

Acute soft head syndrome (ASHS) is a rare complication of sickle cell disease that often requires a high index of suspicion and is often a diagnosis of exclusion. We present the case of an 18-year-old male with sickle cell disease in the United States who developed acute soft head syndrome without known traumatic injury. The goal of this case presentation is to provide awareness and education regarding a rare complication of sickle cell disease and recommended management for the associated symptoms.

show abstract

Acute Soft Skull Syndrome in an Adult Male with Sickle Cell Anemia in Sudan: A Case Report

Cited by 2 publications

References 17 publications

Acute soft head syndrome in a teenager with sickle cell anemia: A case report

Acute soft head syndrome in a teenager with sickle cell anemia: A case report

Unilateral Facial Swelling in a Sickle Cell Patient

Contact Info

Product

Resources

About