“…The main differential diagnosis is with pseudo-ainhum, an auto-amputation of the digits that results of an identifiable or associated disease process and is independent of race. Two spectra of pseudo-ainhum has been described: the primary pseudo-ainhum, characterized by a congenital condition presented in the first ages [2] as a result of an identifiable or associated process; and the secondary pseudo-ainhum, characterized by presentation in later in life and associated with keratodermia also named Vohwinkel Syndrome [9], trauma, Hansen's disease, scleroderma, atypical keratoderma, syringomelia, syphilis, vascular or diabetic gangrene [3].…”