Airway Growth in Preoperative Patients with Crouzon Syndrome

Lu, Xiaona; Forte, Antonio J.; Park, Kitae Eric; Allam, Omar; Smetona, John; Alperovich, Michael; Steinbacher, Derek M.; Tonello, Cristiano; Alonso, Nivaldo; Persing, John A.

doi:10.1089/fpsam.2020.0441

Cited by 5 publications

(1 citation statement)

References 32 publications

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“…Schafer identified maxillary hypoplasia and narrow posterior choanal openings as the most important factors in the pathogenesis of the upper airway obstruction of children with craniofacial anomalies [ 6 ]. A recent study of airway growth in Crouzon’s syndrome revealed that the reduction in the nasal airway volume would become nearly normal after 6 years of age but that the reduction of the pharyngeal airway volume would remain throughout adulthood [ 7 ]. The degree of improvements in OSAS by creating the nasal cavity alone in this patient with both mid-facial hypoplasia and choanal atresia was unpredictable.…”

Section: Discussionmentioning

confidence: 99%

Surgical treatment of bony nasal airway stenosis in a patient with adult Crouzon’s syndrome

Kamikonya

Inokuchi

Tatehara

et al. 2022

Journal of Surgical Case Reports

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Crouzon’s syndrome is associated with the respiratory impairment of the upper airway due to mid-facial hypoplasia. We managed an adult Crouzon patient who wanted us to treat his choanal and nasopharyngeal stenosis for obstructive sleep apnea relief and tracheostomy tube extubation. We drilled out the abnormal maxillary bone and created a new nasal passage to the pharynx. Epithelialization of the new nasal cavity was completed within a month, and the patient was able to breathe through the nose and his sense of smell improved somewhat after the surgery. Although the apnea-hypopnea index had decreased, sleep apnea remained.

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Section: Discussionmentioning

confidence: 99%