Airway management in a patient with Crouzon syndrome proposed to orthognathic surgery

Fernandes, Melissa; Eufrásio, Ana; Bonifácio, João; Marcelino, J.P.

doi:10.1136/bcr-2017-219371

Cited by 3 publications

(4 citation statements)

References 13 publications

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“…An infant with CS may present mildly, with a slight midface deficiency, or more severely, with fused numerous cranial sutures, and eye issues (16,17). Acute respiratory distress can be brought on by upper airway obstruction (18,19). Increased intracranial pressure leading to optic atrophy may occur, resulting in blindness if not treated (20,21).…”

Section: Discussionmentioning

confidence: 99%

Orthodontic Management of an Adult Crouzon Syndrome: A Case Report

Sobouti

Dadgar

Salehabadi

et al. 2022

Preprint

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Section: Discussionmentioning

confidence: 99%

Orthodontic Management of an Adult Crouzon Syndrome: A Case Report

Sobouti

Dadgar

Salehabadi

et al. 2022

Preprint

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“…The published literature with respect to anesthetic airway management of children with Crouzon or Pfeiffer syndrome is largely limited to single case reports 6–8 . Perioperative airway management in these patients is challenging for a number of reasons.…”

Section: Discussionmentioning

confidence: 99%

“…To our knowledge, there is currently no large, published case series of perioperative airway complications and management in patients with Crouzon and Pfeiffer syndromes. Most of the current published literature is limited to single case reports relating to anesthetic management 6–8 or larger series focusing on craniofacial surgical complications 9,10 …”

Section: Introductionmentioning

confidence: 99%

Perioperative airway complications in infants and children with Crouzon and Pfeiffer syndromes: A single‐center experience

Raman

Beer

2021

Pediatric Anesthesia

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Background Crouzon and Pfeiffer syndromes are rare genetic disorders characterized by craniosynostosis, exorbitism, and maxillary hypoplasia. Patients with these syndromes frequently require general anesthesia for various diagnostic and surgical procedures and may present a challenge to anesthetists with regard to airway management. Aims The primary aim of this study was to determine the incidence, timing, and management of perioperative upper airway obstruction in infants and children with Crouzon and Pfeiffer syndromes. The secondary aim was to determine the degree of difficulty in performing endotracheal intubation. Methods A retrospective review of 812 anesthetic encounters in 67 patients was conducted. The following were recorded: timing and management of episodes of perioperative upper airway obstruction, from induction of anesthesia to discharge from recovery, degree of difficulty with laryngoscopy using the Cormack‐Lehane grading system and number of intubation attempts required, patient demographics, respiratory comorbidity, surgical procedure, and anesthetic airway management techniques. Results Upper airway obstruction at induction of anesthesia was very common, with an incidence of 31% (167/542 anesthetic encounters affecting 54 patients). In a quarter of these incidents, bag‐valve‐mask ventilation was challenging, but a laryngeal mask airway was almost always effective. Upper airway obstruction on emergence from anesthesia was less common, with an incidence of 2.7% (14/515 anesthetic encounters affecting 10 patients). Contributing factors included patient comorbidity (obstructive sleep apnea, nasal stenosis) and the nature of surgery (craniofacial or airway procedures). Intubation was rarely difficult in this cohort, with 85% of laryngoscopies rated Cormack‐Lehane grade 1 or 2 (n = 373), and 89% of intubations successful on the first attempt (n = 306). Conclusions Upper airway obstruction at induction of anesthesia is common in patients with Crouzon and Pfeiffer syndrome. These patients are likely to present some difficulties with perioperative airway management, especially bag‐valve‐mask ventilation, but rarely endotracheal intubation.

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“…Для этого раскрывают рано заращенные швы черепа и исправляют форму лица. В настоящее время в хирургическую практику внедряются дистракционные методики коррекции деформаций лицевых костей с помощью специальных аппаратов для смещения участка черепа и исправления костных дефектов [2,[32][33][34][35][36][37][38].…”

Section: Discussionunclassified

Crouzon Syndrome: Clinical case

et al. 2019

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Relevance. Crouzon syndrome is a craniostenosis due to combination of cranial bones hypoplasia and premature ectocranial sutures fusion resulting in deformation of cerebral and facial cranium. Deformations of facial cranium are responsible for exophthalmos and corneoconjunctival xerosis and can lead to spontaneous eyeball dislocation. Clinical case description. The clinical case of bilateral eyeball dislocation in a patient (right eye at the age of 1 year 2 months, left — at 1 year 4 months) due to untimely original reconstructive surgery is presented. The blepharorrhaphy and osteotomy of cranio-orbital-zygomaxillary complex with installation of two distraction correction instruments on maxillary bone and two on frontal bone, distance osteogenesis, fronto-temporal region remodelling were performed at the age of 3 years 2 months. Conclusion. Crouzon syndrome is incurable illness that demands timely functional and cosmetic correction. Prognosis for this disease is unfavourable. These days the child is 8 years old: physical development delay and mental retardation progression as well as psychoneurological disorders are recorded.

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Airway management in a patient with Crouzon syndrome proposed to orthognathic surgery

Cited by 3 publications

References 13 publications

Orthodontic Management of an Adult Crouzon Syndrome: A Case Report

Orthodontic Management of an Adult Crouzon Syndrome: A Case Report

Perioperative airway complications in infants and children with Crouzon and Pfeiffer syndromes: A single‐center experience

Crouzon Syndrome: Clinical case

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