Albumin Metabolism in Cystic Fibrosis

Pittman, Fred E.; Denning, Carolyn R.; Barker, Harold G.

doi:10.1001/archpedi.1964.02090010362005

Cited by 3 publications

(1 citation statement)

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“…Hypoproteinemia has been seen in cystic fibrosis from secondary volume expansion due to cor pulmonale 13 and in cases of advanced biliary cirrhosis. Severe liver dysfunction may also result in reduced albumin synthesis.…”

Section: Discussionmentioning

confidence: 99%

Edema, Anemia, Hypoproteinemia, and Acrodermatitis Enteropathica

Muñiz

Bartle

Foster

2004

Pediatric Emergency Care

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Cystic fibrosis is a genetic disorder characterized by chronic obstructive pulmonary disease, pancreatic exocrine deficiency, and abnormally high sweat electrolyte concentrations. Less frequently, the presenting features in infants may include edema, anemia, hypoproteinemia, and acrodermatitis enteropathica. Liver involvement may produce hepatomegaly and mild elevation of transaminases. This clinical symptom usually presents within the first 6 months of life and is associated with a high morbidity and mortality. Early recognition and institution of appropriate nutritional supplementation and pancreatic enzymes is essential to improve outcome. Since the sweat test may be falsely negative, emergency physicians must maintain a high index of suspicion to make the diagnosis of cystic fibrosis in an infant who presents with edema, anemia, hypoproteinemia, and acrodermatitis enteropathica.

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Section: Discussionmentioning

confidence: 99%