Amyloid cerebrovasculopathies

Scolding, Neil

doi:10.1136/practneurol-2022-003386

Cited by 1 publication

(1 citation statement)

References 11 publications

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“…9 Immunosuppressive agents like azathioprine, methotrexate and mycophenolate may be used as maintenance therapy, with the latter appearing to be the least effective of the three. 10 Our patient was given IV methylprednisolone 1g/day for five days followed by a tapered regimen of oral steroids to which he showed significant improvement, as explained earlier. The outcome is favorable when treated with a combination of steroids and cyclophosphamide.…”

Section: Discussionmentioning

confidence: 74%

Primary angiitis of the central nervous system presenting as sudden vision loss in a young patient

Khan,

Jafri,

Shafqat

2023

PJNS

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Primary angiitis of the central nervous system is a rare disorder that primarily affects the cerebral vessels and can prove to be a diagnostic challenge to the clinicians. It can present with a variety of clinical manifestations and lacks the evidence of any systemic disease. Digital subtraction angiography is often necessary to confirm the diagnosis of cerebral vasculitis but in cases where it may fail to do so, brain biopsy is eventually required. Obliviousness to this condition may lead to false management strategies and hence it is imperative to make an accurate diagnosis to facilitate proper treatment that mainly includes a combination of steroids and immunosuppressive agents. We report a case of a 27-year-old male with sudden bilateral vision loss who underwent extensive workup and was ultimately diagnosed with primary angiitis of the central nervous system. He was treated with steroids and responded well to it.

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Section: Discussionmentioning

confidence: 74%