Amyloid diseases of the heart: assessment, diagnosis, and referral

Dubrey, Simon W; Hawkins, PN; Falk, R. H.

doi:10.1136/hrt.2009.190405

Cited by 180 publications

(202 citation statements)

References 19 publications

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“…A amiloidose AL pode coexistir com mieloma múltiplo em 10-15% dos casos e geralmente o prognóstico é ruim. 3 Nas outras duas formas de amiloidose a proteína precursora é a transtirretina. A amiloidose secundária resulta de uma produção excessiva de imunoglobulina conhecida como AA 2 e é tipicamente consequente de condições in-flamatórias crônicas, como artrite reumatóide, doença de Crohn e outras doenças inflamatórias/infecciosas.…”

Section: Introductionunclassified

Cardiac cmyloidosis: case report

Carvalho

Rodrigues

Vitório

2017

Medicina (Ribeirão Preto)

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RESUMOA amiloidose é resultante do depósito extracelular de proteínas séricas (amiloide) e pode acometer quase todos os órgãos. A amiloidose cardíaca é uma cardiomiopatia geralmente progressiva que apresenta prognóstico reservado. Neste relato apresentamos um paciente com sinais e sintomas de insuficiência cardíaca e hipertrofia ventricular esquerda, que devido ao diagnóstico tardio de amiloidose cardía-ca, acabou evoluindo a óbito. Assim, esta doença deve ser sempre considerada na ausência de outra causa que justifique tais achados. Palavras-chave:Amiloide. Insuficiência Cardíaca. Sinais e Sintomas. ABSTRACTAmyloidosis is a result of the extracellular deposit of seric proteins (amyloid) and almost all organs can be compromised. Cardiac amyloidosis is usually a progressive cardiomyopathy that has a bad prognosis. We present here a case report about a patient that had signs and symptoms of heart failure and left ventricle hypertrophy. Because it was not possible to make the diagnosis of cardiac amyloidosis in time, he died. This disease must be considered when no other cause for those findings exists.

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Section: Introductionunclassified

Cardiac cmyloidosis: case report

Carvalho

Rodrigues

Vitório

2017

Medicina (Ribeirão Preto)

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“…MRI of the heart can show global gadolinium late enhancement in a subendocardial distribution that is highly sensitive and specific for the identification of cardiac involvement. 48 [ 123 I]metaiodobenzylguanidine may help to detect cardiac sympathetic denervation. 49 Aprotinin scintigraphy has been used successfully for the identification of cardiac involvement in AL amyloidosis.…”

Section: Imaging Of Amyloidosismentioning

confidence: 99%

Amyloidosis

Hazenberg

2013

Rheumatic Disease Clinics of North America

139

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“…Cardiac amyloidosis is a progressive infiltrative cardiomyopathy characterized by restrictive cardiomyopathy and presentation with conduction system diseases (1). Patients with cardiac amyloidosis due to the senile form of amyloidosis have few causal treatment options.…”

Section: Introductionmentioning

confidence: 99%

Multidisciplinary Mechanical Supports Improve Outcome in a Shock Patient with Cardiac Amyloidosis: A Case Report

et al. 2012

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Shock patients with restrictive cardiomyopathy due to cardiac amyloidosis are refractory to medical treatment. Here, we report a case of early initiation of intra-aortic balloon pumping (IABP) in a patient with cardiac amyloidosis who developed postoperative shock. Continuous hemodiafiltration was also applied to control circulating fluid volume. The mechanical treatments allowed reduction of the doses of catecholamine and diuretics and resulted in full recovery. It is reasonable to initiate IABP and hemofiltration dialysis during the early stages for the appropriate control of hemodynamics and fluid in shock patients with cardiac amyloidosis.

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Amyloid diseases of the heart: assessment, diagnosis, and referral

Cited by 180 publications

References 19 publications

Cardiac cmyloidosis: case report

Cardiac cmyloidosis: case report

Amyloidosis

Multidisciplinary Mechanical Supports Improve Outcome in a Shock Patient with Cardiac Amyloidosis: A Case Report

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