An Atypical Presentation of Myopericytoma in Palmar Arch and Review of the Literature

Abstract

Introduction. Myopericytoma is a very rare perivascular tumor that can be presented with painful mass in lower extremities. We aimed to present an atypical presentation and location of myopericytoma. Presentation of Case. An 18-year-old otherwise healthy individual was admitted to outpatient clinic with complaints of numbness and pain in his right hand. He has had no trauma. On volar aspect of his right hand, a well-circumscribed, painful mass was palpated. MRI results were related to hemangioma. Surgical excision was planned and performed. Pathological investigation revealed the mass is myopericytoma. Discussion. This case demonstrates a rare location and presentation of myopericytoma. Reviewing the literature, discussion was made to expand the horizon for diagnosis and treatment of patients with similar symptoms. Conclusion. Myopericytoma can rarely present with numbness and pain in affected region. Surgical excision is helpful for definitive diagnosis and symptom relief.

Digital Myopericytoma: A Case Report and Systematic Literature Review

“…In previous studies, MP lesions appear lobulated, well circumscribed, and mass enhancing on MR. T1A-and T2A-weighted images demonstrate lowand high-signal intensity, respectively. 11 There are several biopsy modalities for the assessment of tumors presenting in the hand and wrist. These include excisional biopsy, fine needle aspiration (FNA), and core biopsy.…”

Intravascular Myopericytoma in the Heel

“…Recently, in October 2014, Kara et al 30 described “thin-walled vessels with a concentric, perivascular gathering of spindled myoid tumor cells” in hand. Furthermore, the possibility that these lesions may be malignant 4 , 5 suggests that the histopathological study of vascular tumors should include immunohistochemical tests.…”

Miopericitoma del pulpejo del dedo: caso clínico y revisión de la literatura

“…Estas lesiones habitualmente se producen en adultos de edad media y en las extremidades inferiores, aunque pueden surgir en cualquier localización 2 . Tras una búsqueda exhaustiva solo hemos encontrado en la bibliografía indexada en español e inglés otros 4 casos de miopericitomas localizados en la mano [5][6][7][8] .…”

“…Por lo que respecta al estudio con RM y/o ecografía preoperatorias, constituyen pruebas muy poco sensibles e incluso de interpretación errónea, como fue en nuestro caso 9 . El diagnóstico definitivo se efectúa por el estudio histológico del espécimen obtenido tras su exéresis 7 . Nuestro caso coincide plenamente con este hecho, ya que la RM preoperatoria diagnosticó la lesión de tumor glómico.…”

“…Existe una variante maligna de miopericitoma y otra variante intravascular 4 . Los casos recidivantes o malignos de miopericitomas son prácticamente inexistentes, incluso cuando su resección es marginal o incompleta 7 .…”