An Extrarenal Malignant Rhabdoid Tumor Suspected to Originate from the Mesentery in an Adult: Report of a Case

Ohgaki, Masaharu; Higuchi, Atsushi; Chou, Hideyuki; Takashina, Kenichiro; Kawakami, Sadao; Fujita, Yoshihiro; Hagiwara, Akeo; Yamagishi, Hisakazu

doi:10.1007/s10595-002-2518-8

Cited by 5 publications

(1 citation statement)

References 12 publications

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“…Reviewing the cases of MERT in recent 10 years, it was found that ultrasound and abdominal CT scan lacked specificity. There is usually hypoechoic or isoechoic masses by ultrasound , and there is a mass with regular shape, clear boundaries, and uneven density, [11] or a dense wall and necrotic center which were been seen by CT. [3] The tumor can be characterized by imaging, with difficult to distinguish between benign and malignant tumor. The final diagnosis is made by pathological and histological examination.…”

Section: Discussionmentioning

confidence: 99%

Malignant Extrarenal Rhabdoid Tumor Derived from the Greater Omentum: A Case Report and Literature Review

Shao,

Xin,

Han

et al. 2024

Preprint

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Background: Extrarenal malignant rhabdoid tumor (MERT) is a rare and highly metastatic tumor, which is more than 75% of patients dying within 6 months of initial diagnosis of MERT. Due to its rarity in clinical practice, there is no expert consensus or guidelines for the diagnosis, and it often leads to misdiagnosis and delayed treatment. Case: This paper reports a 16-year-old girl who presented with the chief complaint of acute abdominal pain. She underwent laparoscopic exploration and excisional biopsy, then pathological examination and immunohistochemistry revealed “extrarenal malignant rhabdomyoma”. One month after operation, she died of intra-abdominal hemorrhage and multiple organ dysfunction. Conclusion: Reviewing the cases of MERT admitted with acute abdomen reported in the last 10 years, it was found that these patients had a poor prognosis. The surgery and chemotherapy is usually beneficial to prolong the survival time of patients with MERT.

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Section: Discussionmentioning

confidence: 99%