An Incidental Diagnosis of Rheumatic Mitral Stenosis and Secundum Atrial Septal Defect (Lutembacher’s Syndrome) in a Young Woman

Alam, Mashiul; Khaled, Fakhrul Islam

doi:10.1155/2019/9402987

Cited by 6 publications

(3 citation statements)

References 10 publications

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“…A systematic review of the literature showed that to date 25 cases of percutaneous intervention for Lutembacher’s have been published in world literature. 8, 10, 11 Due to the presence of ASD there is a lack of support for the PTMC balloon and hence crossing the mitral valve can be challenging. Various techniques are then required eg.…”

Section: Discussionmentioning

confidence: 99%

Percutaneous Transcatheter Therapy in a Case of Lutembacher’s Syndrome

Nadkarni,

Parab,

Naik

2024

Indian Journal of Clinical Cardiology

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Lutembacher’s syndrome is a rare condition and is most often treated surgically. Due to the advances in percutaneous procedures, this form of management is desired which has the advantage of decreased morbidity and is aesthetically superior. In this case report of percutaneous treatment for a Lutembacher’s patient the percutaneous transvenous mitral commissurotomy and atrial septal defect device closure was done with minimal technical difficulties and with excellent post-procedure results.

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Section: Discussionmentioning

confidence: 99%

Percutaneous Transcatheter Therapy in a Case of Lutembacher’s Syndrome

Nadkarni,

Parab,

Naik

2024

Indian Journal of Clinical Cardiology

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“…Lutembacher syndrome (LS) is an extremely rare clinical condition first reported in 1916 by the French physician Rene Lutembacher, who described a 61-year-old woman with atrial septal defect (ASD) and mitral stenosis (MS) [Mahajan 2020]. LS is defined as any combination of congenital or iatrogenic atrial ASD with congenital or acquired MS [Alam 2019]. The incidence of this disease is extremely low, affecting approximately 0.6% to 0.7% of individuals with MS. Congenital MS combined with congenital ASD is rare and accounts for only 0.6% of all cases of congenital heart disease [Mahajan 2020].…”

Section: Introductionmentioning

confidence: 99%

Surgical Treatment of Lutembacher Syndrome with a Huge Right Atrium: A Case Report

Yang

Zhang

Han

et al. 2021

HSF

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Background: Lutembacher’s syndrome (LS) is a rare cardiovascular anomaly that is defined as any combination of congenital or iatrogenic atrial septal defect (ASD) with congenital or acquired mitral stenosis (MS). The clinical features and hemodynamic effects of LS depend on the balance between ASD and MS. Case Report: In this case report, we describe a rare case of LS with a huge right atrium in a 39-year-old male patient who was admitted to the hospital with worsening fatigue and breathlessness on exertion. Clinical examination revealed central cyanosis, raised jugular venous pressure bilaterally, clear breath sounds bilaterally with no dry and wet rales, hyperdynamic apex beat, and dull heart sounds. His vital signs on admission included blood pressure of 90/60 mmHg, irregular pulse of 76 beats/min, and oxygen saturation of 90.4%. Echocardiography revealed moderate to severe MS with ASD (ostium secundum). The patient’s condition deteriorated after initial medical management, and he underwent open heart surgery for mitral valve replacement, ASD repair, tricuspid annuloplasty, and right atrial volume reduction. Conclusions: This case report describes the successful surgical management of this rare condition.

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“…3 They can also present with signs and symptoms of right heart failure because of pulmonary hypertension, such as jugular engorgement, systolic murmur in the pulmonic valve area, and systolic murmur in the tricuspid valve area. 3,5 Patients will ultimately develop Eisenmenger syndrome (ES) because of increased pulmonary vascular resistance. The initial left-to-right shunt will become a right-toleft shunt, resulting in significant hypoxemia and cyanosis, and worsening their prognosis.…”

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confidence: 99%