An Interesting Case of Langerhans Cell Histiocytosis Involving the Vulva and the Cranium

Abstract

Background: Vascular tumors and malformations are rare among the vascular anomalies that affect the female external genitalia. Of the vascular tumors, hemangiomas are the most common lesions. Cavernous hemangiomas are less common then capillary hemangiomas, typically regressing completely by age 5 in 80% of patients. 1 Hemangiomas in general are asymptomatic. The clinical presentation of both vascular tumors and malformations is highly variable. The diagnosis depends on the clinical presentation and radiologic imaging. MRI is used to determine the extent of the lesions and their relationship to adjacent structures. Doppler ultrasound is often necessary to distinguish between a hemangioma and a vascular malformation. Vascular malformations are generally treated with sclerotherapy or embolization. Vascular tumors that enlarge, fail to regress, or if the patient complains of bleeding or discomfort usually require surgical excision.