An uncommon long-term survival case of primary cardiac leiomyosarcoma

Abstract

Primary cardiac sarcoma is a rare aggressive entity. It constitutes the second most common type of primary cardiac neoplasms. Its management has largely been guided by small retrospective series with a median survival of 6 months. Here, we discuss a unique case of 8-year survival cardiac leiomyosarcoma managed by surgical and adjuvant therapy.

Biatrial High-Grade Leiomyosarcoma With Nine-Year Post-Surgical Survival

“…Despite having a large tumor with pathologically poor prognostic features, our patient is doing well 9 years after therapy. With 2 patients with 7 and 8 years [6] of survival recently reported in the literature, and our patient's 9-year survival, we suggest that long-term survival following treatment for primary cardiac leiomyosarcoma…”

Primary Cardiac Leiomyosarcoma: A 27-Month Survival with Surgery and Chemotherapy

“…Table shows similar cases that survived for over 24 months with the available data regarding treatment modalities and outcome ( 12 - 28 ). A long survival was reported 17 cases.…”

Multimodality imaging of a recurrent case of right-sided cardiac leiomyosarcoma with an unusual clinical course

“…Although most patients die within 1 year of diagnosis, Glaoui et al have reported an 8-year survival duration after combined surgical and adjuvant radiochemotherapy. [4] While echocardiography is currently a widely-used method for diagnosing cardiac masses, differential diagnosis of cardiac tumors often presents a challenge for the sonographer. When malignancy is suspected, MRI and CT remain essential for operative planning and identification of tumor extension.…”