An uncomplicated pregnancy associated with Sturge–Weber angiomatosis

Anaesthesia for caesarean section in a patient with Sturge–Weber syndrome following acute neurological deterioration

“…Seizures may be complex or partial motor and frequently manifest on the side contralateral to the intracranial lesions. 5 Management of anaesthesia in our case was challenging. Lesions in SWS consist of intracranial vascu- There is a lesion in the right parieto-occipital area consistent with a small angioma within the parenchyma of the brain.…”

Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

“…Cardiac abnormalities are rare in SWS but septal defects, valvular lesions and transposition of the great vessels have been reported, and should be ruled out. 15 In case reports of SWS in pregnancy, the predominant mode of delivery (when the information is given) is by CS 9,10,17–19 often prompted by neurological deterioration or concerns, but influenced by maternal request in one case. 18 In one woman who had a small intraventricular haemorrhage four days post-delivery, labour had been induced, followed by a CS at full dilatation.…”

Sturge-Weber Sendromlu Olguda Anestezi Yonetimi

“…Serebrovasküler olaylara benzeyen ataklar, serebral sinüs trombozu, intrakraniyal hemoraji, subaraknoid kanama, nöbetler ve migren karışabilecek tanılardır. Tromboz nedeniyle aspirin ve antikoagülan kullanan hastalarda rejyonel anestezi uygulamaları, spinal ve epidural hematom gelişme riski açısından bir risktir (2). Sunulan olguda serebral atrofi, serebrovasküler iskemi ve hemoraji, intrakraniyal hemoraji, nöbet ve migren öyküsü yoktu, aspirin ve antikoagülan da kullanmamakta idi.…”

“…Sendrom; göz, deri ve santral sinir sistemini farklı zamanlarda etkileyebilen ağız bölgesi yumuşak dokuları, çene yüz ve leptomeninkslerin venöz anjiomalarının kombinasyonlarıyla karakterizedir (1,2). Leptomeningeal hemanjiomlar trigeminal sinir bölgesine dağılmış genellikle tek taraflı Porto şarabı nevuslerle karakterizedir.…”