An unusual case of rhabdomyosarcoma presenting as orbital apex syndrome

Indications for image-guidance in pediatric sinonasal surgery

“…Differences in preoperative setup times may be explained by the fact that our times pertain to the overall OR setup, and not specifically to the efforts spent on the IGS system setup alone [24,26,27]. Indications for the use of IGS have expanded from merely visual assistance in revision polyposis and sinus surgery with missing critical landmarks, to actual and active navigation guidance in frontal sinus osteoplastic flaps, optic nerve decompression and select sinonasal and anterior cranial base tumors, as well as initial procedures for polyposis in cystic fibrosis, bone resection in choanal stenosis, recurrent JNA, and tumor biopsy [11,12,22,28].…”

Solid Variant of Alveolar Rhabdomyosarcoma of Nasal Cavity

“…8,10,12 In adults, the uncommon manifestations reported in literature are metastatic disease in the temporal bone, meninges, lungs, mediastinum, bones, pancreas, right ovary and orbital apex syndrome. 5,8,11,13 CECT and MRI aids in radiological diagnosis. CT imaging is done to evaluate the primary tumor and define the surrounding vital structures as well as to look for any bone erosion.…”

“…Alveolar rhabdomyosarcoma are seen to stain strong positive for desmin, myogenin, MSA, vimentin and MYOD1 in immunohistochemistry. 9,13 Treatment is by surgical excision, radiotherapy, chemotherapy or a combination of these. Adequate resection is said to have achieved by resecting 0.5 cm of normal tissue around the tumor mass.…”

Orbital Apex Syndrome: A Rare Form of Ophthalmic Zona: Case Report

“…1,3,4,[7][8][9][10][11][12][13][14][27][28][29] Çocuklarda rabdomiyosarkom, nöroblastom ve retinoblastomun orbita metastazları en sık nedenler arasındadır. 4 Orbital apeks sendromunun etiyolojisinde enfeksiyon etkenlerine de sık rastlanır. Öncelikle orbital apeksin kompresif apseleri, orbitanın veya kavernöz sinü-sün mantar enfeksiyonları bu sınıftandır.…”

“…[1][2][3] Orbital apeksi oluş-turan yapıların, yani superior orbital fissür ile optik kanalın tutulmasıyla klinik tablo gelişir. 4 Bu sendrom, çoğunlukla ya orbital apeksin benin veya malin neoplazisine veya yüzün masif travmalarına sekonder olarak ortaya çıkar. 4 Kompresyon yapan lokal bir apse, yangısal süreçler, meninkslerin veya santral sinir sisteminin enfeksiyonu da benzer şekilde etiyolojide rol Orbital Apeks Sendromu: Nadir Bir Oftalmik Zoster Şekli Ö ÖZ ZE ET T Orbital apeks sendromu görmede azalma, oftalmopleji, blefaropitoz, ekzoftalmus ve alın ve üzt dudakta anestezinin birlikte görüldüğü bir durumdur.…”