An unusual case of Shone's complex in an adult depicted on computed tomography angiography

Abstract

We present a case of a 22‐year‐old male with dyspnea on exertion where computed tomography revealed complete Shone's complex. This case highlights the complementary role of computed tomography in the anatomical evaluation of patients with complex heart diseases.

Echocardiography to the Rescue in Adult-Onset Partial Shone Complex

“…The severity of MS is the most important indicator of mortality and long-term prognosis. 3 In a retrospective study of 50 Shone complex patients, certain MV morphologies (thickened leaflets, shortened MV chordae, and turbulent flow below the MV plane) were associated with significant MS and poor outcomes. 4 Classically, the MV morphology associated with Shone complex is that of a true parachute MV and a supramitral ring.…”

“…Often, in adult patients with Shone complex such as ours, the first presenting symptom is dyspnea on exertion. 3 The degree of dyspnea and disability is proportional to the degree of MS from the structurally abnormal MV. Indeed, MV obstruction and stenosis is thought to be the first pathological event in this syndrome.…”