Anesthetic and Dental Management of a Child With IMAGe Syndrome

Abstract

IMAGe syndrome (OMIM 300290) is a rare multisystem disorder that has a broad phenotypic presentation. Though variable, this disorder mainly consists of Intrauterine growth retardation, Metaphyseal dysplasia, Adrenal hypoplasia congenita, and Genital abnormalities. Patients with IMAGe syndrome present as an uncommon yet important challenge for dentists and anesthesiologists due to their wide range of dysmorphic facial features, adrenal insufficiency, electrolyte imbalances, and need for steroid replacement. The purpose of this case report is to describe the successful anesthetic management of a pediatric patient diagnosed with IMAGe syndrome who presented for full mouth dental rehabilitation.

Displacement of deciduous tooth into hypopharynx due to endotracheal intubation

“…Thus, the teeth in the upper anterior region must be assessed before and after intubation for general anesthesia [ 2 6 ]. The possibility of damage to a tooth, such as a fracture, and/or dislocation must be considered when using general anesthesia in children [ 7 8 ].…”