Anesthetic considerations in a parturient with congenital insensitivity to pain with anhidrosis

Pirani, Zameer; Qasem, F.; Katsiris, Sandra

doi:10.1016/j.ijoa.2016.10.005

Cited by 4 publications

(2 citation statements)

References 8 publications

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“…The need for perioperative opioid administration in CIPA patients is still controversial. According to current literature, some patients can be operated on while sedated 12 ; however, it is believed that while these patients are insensitive to pain, paradoxically, they may have hyperalgesia. Some CIPA cases have reported perioperative somatotropic reactions caused by increasing surgical stimulation and postoperative pain complaints 13,14 .…”

Section: Discussionmentioning

confidence: 99%

A case report: Anesthetic management for open‐heart surgery in a child with congenital insensitivity to pain with anhidrosis

Jiang

Wang

et al. 2022

Pediatric Anesthesia

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Congenital insensitivity to pain with anhidrosis (CIPA) is a rare disease also known as hereditary sensory and autonomic neuropathy. CIPA is characterized by a lack of pain sensitivity and impaired development of sweat glands. Surgery is required for patients with self-mutilation and skeletal developmental disorders. Due to the disease's rarity and intricacy, anesthesia poses its challenges. Although there have been a few cases of CIPA patients receiving surgery and anesthesia, the number is very limited. Here, we report a case of a child with CIPA who underwent open-heart surgery and discuss the anesthetic considerations. We conclude that patients with CIPA undergoing openheart surgery require some opioids, that muscle relaxants and volatile anesthetics should be used with extreme caution, and that airway management and temperature control require special attention.

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Section: Discussionmentioning

confidence: 99%

A case report: Anesthetic management for open‐heart surgery in a child with congenital insensitivity to pain with anhidrosis

Jiang

Wang

et al. 2022

Pediatric Anesthesia

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“…For patients who can cooperate, neuraxial anesthesia can be used for abdominal and lower extremity surgeries. Pirani et al ( 7 ) reported that a parturient with CIPA successfully underwent neuraxial anesthesia for cesarean delivery. Our patient had intellectual disability, was irritable, and was unable to cooperate, so we ultimately chose general anesthesia for this diagnostic procedure.…”

Section: Discussionmentioning

confidence: 99%

Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report

Zhang

Geng

2022

Front. Surg.

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Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disease classified as hereditary sensory and autonomic neuropathy type VI. Patients with CIPA are characterized by insensitivity to pain, episodes of unexplained fever, anhidrosis, self-mutilating behavior, intellectual disability, and autonomic nervous system abnormalities. The clinical features may intrinsically pose anesthetic challenges. We present a case of a patient with CIPA who underwent tumor biopsy under general anesthesia using a Supreme laryngeal mask airway without any complications. The anesthetic management of this condition is discussed.

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Pregnancy in hereditary sensory and autonomic neuropathy type V: A case report and literature review

Higeta

Morita

Uehara

et al. 2022

Taiwanese Journal of Obstetrics and Gynecology

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Anesthetic considerations in a parturient with congenital insensitivity to pain with anhidrosis

Cited by 4 publications

References 8 publications

A case report: Anesthetic management for open‐heart surgery in a child with congenital insensitivity to pain with anhidrosis

A case report: Anesthetic management for open‐heart surgery in a child with congenital insensitivity to pain with anhidrosis

Anesthetic management of a child with congenital insensitivity to pain with anhidrosis: A case report

Pregnancy in hereditary sensory and autonomic neuropathy type V: A case report and literature review

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