Anesthetic Management of Abdominal Aortic Aneurysm Repair in a Patient With Tuberous Sclerosis Complex

Abstract

Tuberous sclerosis complex, also known as Bourneville disease, is an autosomal dominant, progressive neurocutaneous disorder with variable presentation and multisystem involvement. It is characterized by the development of benign tumors in multiple organs and tissues in the body, with the majority of patients having neurological involvement. We report a 19-year-old adolescent, with tuberous sclerosis and advanced systemic involvement of the disease, presenting for surgical repair of an abdominal aortic aneurysm. The etiology and presentation of TS are discussed and its multisystem organ involvement is reviewed with emphasis on the anesthetic implications of the disease.