Anesthetic Management of Congenital Insensitivity to Pain with Anhidrosis in a Child: A Case Report

Abstract

Background: Congenital insensitivity to pain with anhidrosis (CIPA) is a rare hereditary sensory autonomic neuropathy. Anesthetic management of those patients is challenging for anesthesiologist because of the potential risks for them including regurgitation and aspiration, sympathetic nervous dysfunction, mandibular osteomyelitis as well as hyperthermic events.