Anesthetic Management on a Patient with Friedreich's Ataxia

Özgül, Ülkü; Erdoğan, Mehmet Ali; Aydoğan, Mustafa Said; Korkmaz, Mehmet; Nakir, Hamza; Durmuş, Mahmut

doi:10.5455/medscience.2013.02.8083

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2014

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“…The involvement of the central and peripheral nervous system would also theoretically make these patients sensitive to the effects of non-depolarizing NMBAs. Alternatively, endotracheal intubation can also be accomplished without the use of a NMBA with agents such as propofol in combination with either sufentanil or remifentanil [15,16]. In our patient, we used rocuronium to facilitate endotracheal intubation.…”

Section: Discussionmentioning

confidence: 99%

Perioperative Management of an Adolescent With Friedreich’s Ataxia and Hypertrophic Cardiomyopathy

Kamata

2014

J Med Cases

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Friedreich's ataxia (FA) is an autosomal recessive neurodegenerative disorder with an incidence of 1:50,000 which usually presents during adolescents. Given the progressive neurologic involvement, surgical intervention is frequently required for correction of orthopedic sequelae including scoliosis. Associated co-morbid conditions including hypertrophic cardiomyopathy, restrictive lung disease, and diabetes mellitus may impact the perioperative care of such patients. We present a 14-year-old girl with FA presenting for posterior spinal fusion for the treatment of scoliosis. The perioperative management of such patients is discussed.

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Section: Discussionmentioning

confidence: 99%