Aneurysms due to intimomedial mucoid degeneration

Abdool-Carrim, A.T.O.; Robbs, J V; Kadwa, A.M.; Kenoyer, G.; Cooper, Kumarasen

doi:10.1016/s1078-5884(96)80079-7

Cited by 16 publications

(46 citation statements)

References 11 publications

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“…The first description came from Gsell and Erdheim (Germany) who linked spontaneous aortic dissections with microscopic features of aortic media degeneration. These observations were soon confirmed in the USA [11]. As the knowledge of the distinct microscopic changes in CMN grew, it became apparent that it might involve different parts of vascular system.…”

Section: Discussionmentioning

confidence: 90%

Spontaneous rupture of abdominal aorta — an unusual manifestation of an idiopathic cystic medial necrosis (Gsell-Erdheim syndrome) and literature overview

Łukasiewicz¹,

Marszałek

2016

Acta Angiologica

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In this report, a case of a male, 40-year-old patient who suffered from spontaneous rupture of undilated abdominal aorta, a manifestation of idiopathic cystic media necrosis (Gsell-Erdheim syndrome), is presented. Spontaneous ruptures of medium-to-large arteries observed in this syndrome are a consequence of elastic fibres degeneration and glucose-amino-glycans (GAG) depositions in the arterial media. Gsell-Erdheim syndrome is also observed in a large

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Section: Discussionmentioning

confidence: 90%

Spontaneous rupture of abdominal aorta — an unusual manifestation of an idiopathic cystic medial necrosis (Gsell-Erdheim syndrome) and literature overview

Łukasiewicz¹,

Marszałek

2016

Acta Angiologica

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“… 1 - 4 Although the condition was initially thought to involve only the aorta, subsequent publications have reported IMMD to affect the major branches of the aorta, as well as smaller vessels such as the coronary and brachial arteries. 1 , 5 , 6 - 8 The aneurysms in IMMD usually have a saccular or fusiform morphology and cause symptoms related to the location of the aneurysm. 6 , 8 …”

Section: Introductionmentioning

confidence: 99%

“… 1 , 5 , 6 - 8 The aneurysms in IMMD usually have a saccular or fusiform morphology and cause symptoms related to the location of the aneurysm. 6 , 8 …”

Section: Introductionmentioning

confidence: 99%

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Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult

Viljoen

Szymanski

Osman

et al. 2016

CVJA

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Intimomedial mucoid degeneration (IMMD) is characterised by aneurysm formation following mucin deposition in the intima and media, with elastic tissue degeneration of the arterial wall. We present a case of a young adult who developed a diffusely aneurysmal aorta and its major branches, which was histopathologically confirmed as intimomedial mucoid degeneration, and a review of the literature. This case report attempts to raise the awareness of the reader to this rare cause of aortic aneurysm and to the bleeding diathesis associated with IMMD that may complicate surgery.

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“…Intimomedial mucoid degeneration is a well described cause of aneurysmal disease occurring almost exclusively in black African women 1. These aneurysms often reach large sizes before rupture and characteristically are noted to have scant thrombus and clot within the aneurysm sac.…”

mentioning

confidence: 99%

Giant abdominal aortic aneurysm secondary to intimomedial mucoid degeneration

Woolgar¹

2001

Postgraduate Medical Journal

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Aneurysms due to intimomedial mucoid degeneration

Cited by 16 publications

References 11 publications

Spontaneous rupture of abdominal aorta — an unusual manifestation of an idiopathic cystic medial necrosis (Gsell-Erdheim syndrome) and literature overview

Spontaneous rupture of abdominal aorta — an unusual manifestation of an idiopathic cystic medial necrosis (Gsell-Erdheim syndrome) and literature overview

Intimomedial mucoid degeneration causing aortic and renal artery aneurysms in a young adult

Giant abdominal aortic aneurysm secondary to intimomedial mucoid degeneration

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