Angéite givrée : une manifestation rare de la fièvre méditerranéenne familiale

Belfaiza, Soukaina; Zerrouk, R.; Brarou, H.; Jeddou, I.; Abdellaoui, Taoufik; Mouzari, Yassine; Laasri, F.; Karim, Rezaul; Oubaaz, A.

doi:10.1016/j.jfo.2020.06.036

Cited by 3 publications

(2 citation statements)

References 6 publications

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“…Retinal involvement in FMF is rare, with a few reported cases of exudative retinal detachment, epiretinal membrane (ERM), 4 retinal tears requiring barrier laser, 7 neovascularization elsewhere requiring panretinal photocoagulation, 4 and vasculitis manifesting as FBA and retinal artery and vein occlusion. 4,8,13,14,15 Two previously reported cases of retinal vein occlusion (RVO) showed visual improvement, similar to the index case, following steroid treatment. The first case was of a 39-year-old man who presented with unilateral FBA-associated central RVO.…”

Section: Discussionmentioning

confidence: 57%

“…There are a few case reports of anterior, posterior, and intermediate uveitis, frosted branch angiitis (FBA), acute posterior multifocal placoid epitheliopathy, episcleritis, scleritis, and panuveitis. 4 , 5 , 6 , 7 , 8 , 9 , 10 , 11 , 12 , 13 , 14 , 15 Due to the plethora of clinical manifestations, some of these cases can be misdiagnosed and pose therapeutic challenges. 16 In this case report, we present the long-term follow-up of a young patient with FMF who presented with acute rupture of the outer retinal layers secondary to FBA-associated hemicentral retinal vein occlusion (HCRVO).…”

Section: Introductionmentioning

confidence: 99%

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Outer Retina Rupture from Subretinal Blood with Spontaneous Sealing and Visual Recovery in Frosted Branch Angiitis from Familial Mediterranean Fever: A Case Report

Vofo¹,

Amer²

2022

tjo

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Familial Mediterranean fever (FMF) is a rare autoinflammatory disorder. Ocular involvement is rare. The full spectrum and response to treatment is poorly understood. An 18-year-old girl previously diagnosed with FMF presented with sudden loss of vision in the left eye (LE). Best-corrected visual acuity (BCVA) in the LE was finger counting at 1.5 meters. Angiitis with mild “frosting,” hemi-central retinal vein occlusion (HCRVO), and acute outer retina rupture (ORR) were observed in the LE. Systemic steroids were initiated immediately. The ORR was sealed 2 weeks later while vision improved to 6/15 (near vision: J2) 5 months later. No recurrences were observed over 5 years of follow-up. We report a rare manifestation of frosted branch angiitis with concomitant HCRVO and ORR in a young patient with FMF. Closure of ORR was attained and vision recovered after treatment with high-dose steroids.

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