Angioid streaks of the retina

A rare association between angioid streaks and pattern dystrophy

“…Multimodal evaluation of the posterior segment confirmed that the case was an association of two ophthalmological diseases, AS and adult-onset foveomacular vitelliform dystrophy of the multifocal type. The concomitant presence of AS and PD has been established in the literature and commonly described in patients with pseudoxanthoma elasticum (1) . This diagnosis was excluded for our patient by the medical clinic and dermatology teams.…”

“…Dear Editor, Angioid streaks (AS) are breaks that occur in a calcified and weakened Bruch's membrane (1,2) . Approximately 50% of the cases are idiopathic, whereas other cases present with an associated systemic conditions, most frequently pseudoxanthoma elasticum, Paget's disease, hemoglobinopathies, and Ehlers-Danlos syndrome (1,2) . Generally, they emerge between the second and fifth decades of life, depending on the associated systemic diseases (2) .…”

“…Fundoscopic examination identifies AS bilaterally as reddish-brown, jagged, subretinal lines, with variable caliber, which radiate from the peripapillary region toward the peripheral retina. AS become darker as they develop and may increase in number, diameter, and extent (1,2) . Initially, AS are usually asymptomatic.…”

“…Initially, AS are usually asymptomatic. Visual impairment occurs because of foveal involvement or with choroidal neovascularization (CNV) (1,2) .…”