Angiosarcoma of the Right Atrium with Extension to SVC and IVC Presenting with Complete Heart Block and Significant Pericardial Effusion

Vakili, Hossein; Khaheshi, Isa; Memaryan, Mehdi; Esmaeeli, Shooka

doi:10.1155/2016/3173069

Cited by 3 publications

(2 citation statements)

References 5 publications

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“…Therefore, it is essential to maintain clinical suspicion in the case of pericardial effusion, even if no cardiac masses are found. On the other hand, the transesophageal echocardiogram has a 97% sensitivity identifying cardiac masses [ 14 , 15 ]. Therefore, it is also essential in the follow-up post-cardiac surgery (when surgery is recommended) [ 11 ].…”

Section: Discussionmentioning

confidence: 99%

Primary Cardiac Angiosarcoma: A Rare and Fatal Diagnosis

Gonçalves¹,

Nunes²,

Vieira³

et al. 2021

Cureus

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Primary cardiac angiosarcoma is a rare malignant neoplasm and occurs most frequently in middle-aged males. It has an aggressive nature, with highly variable clinical features, which results in delayed diagnosis and high mortality.We report a 19-year-old man presented to the ED with a three-month history of hemoptysis and one-week history of anterior chest pain. Additionally, an aortic diastolic murmur grade II/VI was found on physical examination. Thoracic CT scan revealed bilateral dispersed hypodense pulmonary nodes with peripheral halo, alveolar densification, and pericardial effusion. The transthoracic echocardiogram confirmed sizeable pericardial effusion and bicuspid aortic valve, without other significant findings. A pericardiocentesis removed 1300 mL of hemorrhagic fluid, consistent with an exudate without malignant cells. Both cardiac magnetic resonance and transesophageal echocardiogram revealed a large mass on the right atrium's anterior wall. Mass biopsy was performed, revealing malignant cardiac angiosarcoma. The biopsy of the lung lesions was compatible with lung metastasis of primary cardiac angiosarcoma. The patient was submitted to palliative chemotherapy but died 12 months after the diagnosis.

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Section: Discussionmentioning

confidence: 99%

Primary Cardiac Angiosarcoma: A Rare and Fatal Diagnosis

Gonçalves¹,

Nunes²,

Vieira³

et al. 2021

Cureus

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“…The chest radiograph plays a pivotal role in the first-line imaging for initial detection of tumors originating from the thorax, although imaging for staging of most cancers is mainly based on CT scan. Regarding mediastinal tumors that could not be identified by chest radiograph, there were case reports on cardiac tumors [2,3], esophageal submucosal tumor [4], and thymus-derived tumors [5,6]. Thymolipoma is known as one of the superimposed thymus-derived tumors [5,6].…”

mentioning

confidence: 99%

Thymic Ccancer Superimposed Opacity of the Mediastinal Anatomical Structures

Uchiyama

Sasatani

Okauchi

et al. 2020

Advances in Respiratory Medicine

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Primary angiosarcoma of superior vena cava: an unexpected diagnosis after an oncological emergency

Salgueiro

Vieira²,

Gomes³

et al. 2021

BMJ Case Rep

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Angiosarcoma (AS) is a rare malignant tumour representing 1%–2% of all sarcomas. Primary AS of superior vena cava (SVC) was reported in two cases worldwide. We report a 69-year-old woman with neck discomfort, headache and dyspnoea for 3 months. CT angiography showed thrombosis in SVC and brachiocephalic veins resulting in an SVC syndrome. The patient began anticoagulant therapy and underwent balloon angioplasty with clinical improvement. Additionally, a positron emission tomography scan confirmed the presence of a mediastinal mass involving the SVC locally. The tumour was excised and a prosthesis was placed on the SVC. Histology revealed a heterogeneous tumour matrix, either myxoid and composed by fusiform cells with vimentin, homogeneous CD31 and a 30% Ki67 immunoexpression, supporting the diagnosis of an AS. Due to multiple complications, the patient never started chemotherapy, and after tumour recurrence, she died within 5 months after diagnosis.

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Angiosarcoma of the Right Atrium with Extension to SVC and IVC Presenting with Complete Heart Block and Significant Pericardial Effusion

Cited by 3 publications

References 5 publications

Primary Cardiac Angiosarcoma: A Rare and Fatal Diagnosis

Primary Cardiac Angiosarcoma: A Rare and Fatal Diagnosis

Thymic Ccancer Superimposed Opacity of the Mediastinal Anatomical Structures

Primary angiosarcoma of superior vena cava: an unexpected diagnosis after an oncological emergency

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