Anomalous drainage of the inferior caval vein to the left atrium

Sierig, Gabriele; Vondrys, David; Dähnert, Ingo

doi:10.1017/s1047951105000181

Cited by 5 publications

(4 citation statements)

References 7 publications

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“…The supra-hepatic segment derives from the right vitelline vein (Oliveira & Martins, 2019). However, if most anomalies of the inferior caval vein can be explained by abnormal development of the different segments, there is no valuable explanation to date for abnormal connection of a right-sided inferior caval vein to the left-sided morphologically left atrium (Sierig et al, 2005).…”

Section: Discussionmentioning

confidence: 99%

“…The most frequent differential diagnosis remains anomalous drainage of inferior caval vein to left atrium, and most of the reported cases could be indeed anomalous drainage rather than anomalous connection. Anomalous drainage is due to an abnormally developed Eustachian valve which fuses with the right edge of the superior interatrial fold (septum secundum) above the oval foramen, redirecting the venous flow from the inferior caval vein to the left atrium through the atrial septum, as demonstrated in some case reports (Genoni et al, 1999;Kogon et al, 2006;Sierig et al, 2005). In that case, the Eustachian valve remains to the right, and the atrial septum to the left, of the inferior caval vein.…”

Section: Discussionmentioning

confidence: 99%

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Prenatal diagnosis of anomalous connection of the inferior caval vein to the left atrium associated with common arterial trunk

Houyel

Cohen²,

Burlot

et al. 2020

Journal of Anatomy

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

Prenatal diagnosis of anomalous connection of the inferior caval vein to the left atrium associated with common arterial trunk

Houyel

Cohen²,

Burlot

et al. 2020

Journal of Anatomy

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“…[9] Another mechanism for the connection of the IVC to the left atrium is the presence of a large Eustachian valve, which can, then, deflect the vein flow through a defect in the oval fossa to the left atrium. [10] Occasionally, this can be mistaken for the lower margin of the defect and closed, diverting blood flow from the IVC to the left atrium. [11] In our case the orifice of the IVC was totally situated in the left atrium and the right inferior pulmonary veins were within the left atrium and away from the orifice of the IVC.…”

Section: Discussionmentioning

confidence: 99%

Inferior vena cava return in left atrium: a rare presentation with severe mitral regurgitation

Chibane¹

2016

Turk Gogus Kalp Dama

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ÖZBu yazıda, klinik tabloyu değiştiren şiddetli mitral yetersizlik ile ilişkili interatriyal iletişimli sol atriyumda inferior vena kavanın anormal bağlantısı olan nadir bir olgu sunuldu. Mitral kapak tamiri ve inferior cava akımının yeniden sağ atriyuma yönlendirilmesinin ardından başarılı bir düzeltme sağlandı.Anah tar söz cük ler: Kardiyak septal defekt; mitral kapak yetersizliği; sinüs venozus atriyal septal defekt; sistemik venöz dönüş. ABSTRACTHerein, we present a rare case of abnormal connection of the inferior vena cava to the left atrium with an interatrial communication associated with severe mitral regurgitation which altered clinical presentation. Successful correction was achieved after mitral valve repair and re-routing of the inferior cava flow to the right atrium.Keywords: Cardiac septal defect; mitral valve insufficiency; sinus venosus atrial septal defect; systemic venous return.Inferior vena cava (IVC) draining into the left atrium is a rare anomaly of systemic venous return. [1][2][3] In the literature, several cases with various anatomical associations have been published. [1][2][3][4][5][6] Herein, we report a female case with a Marfanoid morphotype, presenting with an abnormal return of the IVC into the left atrium associated with an interatrial communication and severe mitral regurgitation. CASE REPORTA 16-year-old schoolgirl was referred for surgical treatment of severe mitral regurgitation associated with an interatrial communication. Physical examination revealed a good overall condition with dyspnea New York Heart Association (NYHA) Class II without cyanosis. Blood pressure was 107/65 mmHg, oxygen saturation 96%, weight 42 kg and height 166 cm. The patient suffered from several phenotypic features mimicking Marfan syndrome; however, she did not fulfill the Ghent's criteria for the definite diagnosis of Marfan syndrome. She presented with skeletal malformations including moderate pectus excavatum, arachnodactyly, joint hypermobility, an arm span to height ratio greater than 1.05; and a decrease in visual acuity. The cardiac examination showed a 3/6 systolic ejection murmur at the apex, split and fixed S2. There was no sign of the right heart failure and all findings were non-specific. Electrocardiography showed a regular sinus rhythm at 8/bpm and biatrial hypertrophy. Chest radiography revealed a cardiothoracic ratio of 0.5 with a prominent pulmonary artery segment and increased pulmonary vascular markings.Echocardiography demonstrated a moderately dilated left ventricle with normal systolic functions and dilated right cavities; an aortic root diameter of 20 mm without regurgitation, Grade 3 mitral regurgitation by A2 and P2 prolapse and trivial tricuspid regurgitation. A low-situated interatrial communication was also diagnosed with significant left to right shunting (QP/QS>2). Computed tomography scan demonstrated a large IVC connecting directly to the floor of left atrium (Figure 1).The patient was operated on by median sternotomy under cardiopulmonary bypass and aortic

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“…Miscellaneous forms of congenital heart disease with direct drainage of hepatic veins into the left atrium have also been associated with pulmonary arteriovenous fistulas. 40,[52][53][54][55][56][57] There are also patients with isolated drainage of the inferior caval vein into the left atrium [58][59][60][61][62][63][64] Some of these patients had pulmonary arteriovenous fistulas, 40,54,57,59 some did not, 56,62,63 and in the others fistulas were not assessed.…”

Section: Abnormal Venous Admixture Cavopulmonary Anastomosesmentioning

confidence: 99%

Normal and abnormal pulmonary arteriovenous shunting: occurrence and mechanisms

Hoffman

2013

Cardiol Young

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Severe cyanosis due to pulmonary arteriovenous fistulas occurs often after a bidirectional superior cavopulmonary anastomosis (Glenn operation) and also in some congenital anomalies in which hepatic venous blood bypasses the lungs in the first passage. Relocation of hepatic flow into the lungs usually causes these fistulas to disappear. Similar pulmonary arteriovenous fistulas are observed in hereditary haemorrhagic telangiectasia, and in liver disease (hepatopulmonary syndrome). There is no convincing identification yet of a responsible hepatic factor that produces these lesions. Candidates for such a factor are reviewed, and the possibility of angiotensin or bradykinin contributing to the fistulas is discussed.

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Anomalous drainage of the inferior caval vein to the left atrium

Cited by 5 publications

References 7 publications

Prenatal diagnosis of anomalous connection of the inferior caval vein to the left atrium associated with common arterial trunk

Prenatal diagnosis of anomalous connection of the inferior caval vein to the left atrium associated with common arterial trunk

Inferior vena cava return in left atrium: a rare presentation with severe mitral regurgitation

Normal and abnormal pulmonary arteriovenous shunting: occurrence and mechanisms

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