Aortic arch anomalies - persistent fifth aortic arch remnant

Edwin, Frank

doi:10.1510/icvts.2010.246462a

Cited by 3 publications

(3 citation statements)

References 5 publications

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“…During normal embryonic development, a total of six aortic arches form asynchronously, and the arch termed as the bilateral fifth arch eventually disappears [ 8 ]. However, in patients with PFAA, the fifth aortic arch fails to degenerate [ 9 ]. PFAA is an extrapericardial structure [ 10 , 11 ].…”

Section: Discussionmentioning

confidence: 99%

Echocardiography of persistent fifth aortic arch confirmed by computed tomography angiography or surgery in children: a case series

Yuan,

Li,

et al. 2024

BMC Cardiovasc Disord

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Background The purpose of this study was to review echocardiography-based diagnosis of persistent fifth aortic arch (PFAA) in children. Methods From January 2015 to December 2022, we retrospectively analyzed the echocardiographic findings and the relevant clinical data during follow-up of patients with PFAA who were treated in the Third Affiliated Hospital of Zhengzhou University. The diagnosis was confirmed by computed tomography angiography or surgery. Results Seven PFAA cases included two Weinberg type A and five Weinberg type B. The anatomical details of PFAA were assessed using a combination of the long-axis view of the left ventricular outflow tract (from the left high parasternal window) and the long-axis view of the aortic arch (from the suprasternal window). In Weinberg type A, the distal fifth and fourth aortic arches were connected to the descending aorta, which was associated with aortic coarctation. In Weinberg type B, the upper arch of the fourth aorta was interrupted, and only the lower arch of the fifth aorta was connected to the descending aorta. Surgical repair of PFAA was indicated in five patients with blood flow disruption, among which four had good postoperative results and one refused surgery. Two patients with unobstructed PFAA blood flow required follow-up rather than surgery. Conclusions It is feasible to diagnose PFAA by echocardiography. Combined application of the high parasternal left ventricular outflow tract view and the suprasternal aortic arch view can improve timely detection of different types of PFAA in children.

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Section: Discussionmentioning

confidence: 99%

Echocardiography of persistent fifth aortic arch confirmed by computed tomography angiography or surgery in children: a case series

Yuan,

Li,

et al. 2024

BMC Cardiovasc Disord

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“…Our research activities have led to several publications (8,9,11,(14)(15)(16)(17) in peer-reviewed journals. We continue to embark on research in other areas.…”

Section: Researchmentioning

confidence: 99%

Paediatric cardiac surgery for a continent – The experience of the Walter Sisulu Paediatric Cardiac Centre for Africa

Kinsley

Edwin

Colsen

et al. 2017

SAHJ

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one congenital heart surgeon for 3.5 million individuals, in Africa the corresponding figure is one congenital heart surgeon for 38 million individuals, making Africa the most underserved continent in terms of congenital heart surgery.(3) To complicate the issue further, the treatment costs related to diagnosis and treatment of CHD is way beyond the means of the largely indigent population.In parts of western Africa, only 20% of the parents of children (less than 15 years old) requiring surgery for congenital cardiac disease are able to finance the operation within 12 months of diagnosis.

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“…Persistent fifth aortic arch (PFAA) is widely recognised as a rare congenital cardiovascular malformation that results from the failure of the fifth aortic arch to degenerate during embryonic development ( 1 ). It was first reported by Van Praagh through autopsy in 1969 ( 2 ).…”

Section: Introductionmentioning

confidence: 99%

Persistent fifth aortic arch: a comprehensive literature review

Huang

Zheng

et al. 2023

Front. Pediatr.

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Persistent fifth aortic arch (PFAA) is an extremely rare congenital cardiovascular anomaly resulting from the failure of the fifth aortic arch to degenerate during embryonic development; it is often associated with various other cardiovascular anomalies. Despite being first reported by Van Praagh in 1969, there have been only a few individual case reports. Owing to its rarity and lack of comprehensive understanding, PFAA is often misdiagnosed or missed diagnosed during clinical. Thus, this review aimed to summarise the embryonic development, pathological classification, imaging diagnosis, and clinical treatment of PFAA to improve its overall understanding, ultimately helping in accurate diagnosis and treatment.

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Aortic arch anomalies - persistent fifth aortic arch remnant

Cited by 3 publications

References 5 publications

Echocardiography of persistent fifth aortic arch confirmed by computed tomography angiography or surgery in children: a case series

Echocardiography of persistent fifth aortic arch confirmed by computed tomography angiography or surgery in children: a case series

Paediatric cardiac surgery for a continent – The experience of the Walter Sisulu Paediatric Cardiac Centre for Africa

Persistent fifth aortic arch: a comprehensive literature review

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