Aortic root replacement in a patient with unoperated tricuspid atresia

Abstract

A 42-year-old man was referred to our hospital with heart failure and unoperated tricuspid atresia with pulmonary valve stenosis. His condition was initially managed with medical therapy; however, he required repeat hospitalisations for congestive heart failure. We diagnosed the chief cause of his heart failure as aortic valve regurgitation secondary to aortic root dilatation. Aortic root replacement was performed and then his heart failure was controlled.

Identification of the atrioventricular conduction axis and its positional relationship with anatomical landmarks of a heart with tricuspid atresia

“… 2 Meanwhile, surgeries for late aortic root dilatation and aortic insufficiency in patients with TA have been recently reported. 3 , 4 , 5 However, the anatomical relationship between the aortic valve and the AVCA in patients with TA has not been elucidated. Our group previously reported the 3-dimensional examination method of the cardiac conduction axis using synchrotron radiation-based x-ray phase-contrast computed tomography (PCCT).…”