Aorto—Right Ventricular Tunnel: A New Concept in Congenital Cardiac Malformations

Aorto–Right Ventricular Tunnel Causing Functional Tricuspid Atresia

“…ARVT is a rare entity thought to represent abnormal formation of the arterial valvar sinuses and leaflets during embryonic development of the outflow tracts, 1 with only 16 patients reported in the English-language literature to date (Table). [2][3][4] We demonstrate a neonate with ARVT in whom both preoperative echocardiography and angiogra- …”

Repair of aortico-right ventricular tunnel

“…This anomaly, similar to the more common aortico-left ventricular tunnel, is believed to be related to a congenital weakness in the region of the right sinus of Valsalva. Associated abnormal origin, or absence, of the right or left coronary ostium has been reported [5,6,8,10]. Hemodynamically, the anomaly produces a left-to-right shunt with resulting pressure and volume hypertrophy of the right ventricle.…”

“…A ventricular septal defect and patency of the ductus arteriosus were excluded. [6] 10 years Absence LCA ostium Survived Jureidini [7] 1 day Normal Died Kleikamp [8] 5 days LCA from ARVT Died Westaby [9] 3 months Normal Survived Rosengart [10] 3 months Absence RCA ostium Died ARVT, aortico-right ventricular tunnel; LCA, left coronary artery; RCA, right coronary artery. The child was operated on without delay.…”

“…In contrast, thus far only 6 cases of aortico-right ventricular tunnel have been reported in the English literature [5][6][7][8][9][10] (Table 1). Of these six patients, five were operated on; only two patients, a 3-month-old infant and a 10-year-old patient, were long-term survivors [5][6][7][8][9][10]. We report a third case of successful surgical closure of this anomaly in a young child.…”

Aortorechtsventrikulärer Tunnel Diagnostik und Therapie einer seltenen Erkrankung

“…ICR links parasternal festgestellt worden. Nur 2, ein 3 Monate alter Säugling und ein 10 Jahre alter Patient, überlebten die Operation [5][6][7][8][9][10][11] Die Symptome einer milden Herzinsuffizienz wurden mit Diuretika behandelt.…”