Aortopulmonary window and aortic isthmic hypoplasia

Tabak, Carol; Moskowitz, William B.; Wagner, Henry R.; Weinberg, Paul M.; Edmunds, L. Henry

doi:10.1016/s0022-5223(19)39186-x

Cited by 15 publications

(3 citation statements)

References 18 publications

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“…For premature and small-for-gestational-age infants, Ghelani et al [ 2 ] advocated two-stage surgery. Premature birth was only reported in four of the Berry syndrome patients we included; of these, 3 underwent two-stage surgery [ 2 , 18 , 24 ], and 1 underwent one-stage surgery [ 46 ]. All of these four patients were alive at the times of final follow-up.…”

Section: Resultsmentioning

confidence: 99%

Berry syndrome: a case report and literature review

Liu

et al. 2021

BMC Cardiovasc Disord

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Background Berry syndrome, a rare combination of cardiac anomalies, consists of aortopulmonary window (APW); aortic origin of the right pulmonary artery; interrupted aortic arch (IAA) or hypoplastic aortic arch or coarctation of the aorta; and an intact ventricular septum. There is lack of review articles that elucidate the clinical features, diagnosis, treatment, and outcomes of Berry syndrome. This publication systematically reviews the 89 cases published since 1982 on Berry syndrome. Case presentation A 38-year-old woman presented with a loud murmur and cyanosis. Transthoracic echocardiography demonstrated a severely dilated aorta and main pulmonary artery with a large intervening defect. Distal to the APW, the ascending aorta gave rise to the right pulmonary artery. Additionally, a type A IAA, an intact ventricular septum, and a large patent ductus arteriosus were revealed. Computed tomography angiography with 3-dimensional reconstruction confirmed above findings. This is the first report of a patient of this age with Berry syndrome who did not undergo surgery. Conclusions Berry syndrome is a rare but well-identified and surgically correctable anomaly. Patients with Berry syndrome should be followed up for longer periods to better characterize long-term outcomes.

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Section: Resultsmentioning

confidence: 99%

Berry syndrome: a case report and literature review

Liu

et al. 2021

BMC Cardiovasc Disord

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“…Two-dimensional and colour Doppler echocardiographic studies can accurately diagnose all the components of Berry syndrome 3 4 Successful surgical repair of this complex heart malformation has been reported in infants and older children using a staged approach; 5 however, with the improvement in surgical techniques, recent case reports have shown better outcome with one-stage surgical correction 6 7…”

Section: Discussionmentioning

confidence: 99%

Berry syndrome: the importance of genetic evaluation before surgical intervention

2015

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“…As for the surgical technique, a two-stage or one-stage repair could be adopted for this cardiac anomaly. In the two-stage approach, closure of AP window comes electively after the reconstruction of aorta with ligation of PDA, 5 while one-stage surgery has all these corrections in a definitive operation. One definitive repair is obviously superior to staged procedures if a patient’s condition is endurable for the surgery, and its results have become favorable without any critical complications these days.…”

Section: Discussionmentioning

confidence: 99%

One-Stage Surgical Repair for Berry Syndrome With Preoperative Diagnosis by 3-Dimensional CT

Morito

Masuzawa

Kobayashi

et al. 2011

World J Pediatr Congenit Heart Surg

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Berry syndrome is a rare congenital combination of an aortopulmonary window, an aortic origin of the right pulmonary artery, an interrupted aortic arch with a patent ductus arteriosus, and an intact ventricular septum. We report a successful one-stage surgical correction of Berry syndrome. Also, we demonstrate the importance of prompt clinical recognition with echocardiography and 3-dimensional reconstruction of computed tomography (3D-CT) and timely operation for the management of this rare cardiac anomaly.

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Aortopulmonary window and aortic isthmic hypoplasia

Cited by 15 publications

References 18 publications

Berry syndrome: a case report and literature review

Berry syndrome: a case report and literature review

Berry syndrome: the importance of genetic evaluation before surgical intervention

One-Stage Surgical Repair for Berry Syndrome With Preoperative Diagnosis by 3-Dimensional CT

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