2013
DOI: 10.1111/dth.12106
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Aplasia cutis congenita: approach to evaluation and management

Abstract: Aplasia cutis congenita (ACC) refers to any condition in which there is absence of skin at birth. This can be isolated ACC occurring on the scalp, with or without underlying ectopic neural tissue, or ACC can be associated with other conditions such as Adams-Oliver syndrome or epidermolysis bullosa. We discuss the different types of ACC and associated anomalies along with an approach to diagnosis and management.

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Cited by 72 publications
(75 citation statements)
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“…When performed, it shows an atrophic epidermis with loose fibrovascular stroma, edematous dermal stroma, or both [5]. A sonography of the lesion and a transfontanellar sonography should be done to rule out skull defects or cerebral abnormalities [7]. BACC can be visualized on prenatal sonography as a smooth cystic lesion without flow [8].…”
Section: Discussionmentioning
confidence: 99%
“…When performed, it shows an atrophic epidermis with loose fibrovascular stroma, edematous dermal stroma, or both [5]. A sonography of the lesion and a transfontanellar sonography should be done to rule out skull defects or cerebral abnormalities [7]. BACC can be visualized on prenatal sonography as a smooth cystic lesion without flow [8].…”
Section: Discussionmentioning
confidence: 99%
“…The decision to use medical, surgical or both modes of therapy depends primarily on size, dept, location of the defects and therapy of associated abnormalities. 5 This child had occlusive honey dressing, but in large defects ACC surgical repair including excision with primary closure, use of tissue expanders and rotation of flap to fill defects, skin and bone grafting may be required.…”
Section: Discussionmentioning
confidence: 99%
“…The treatments of ACC depend primarily on size, dept and location of the defect and therapy of associated disorders. 5 Variety of dressings both adhesive and non adhesive materials have been used. 6,7 Surgical repairs of large defects can be done.…”
Section: Introductionmentioning
confidence: 99%
“…La relación con malformaciones de cráneo y sistema nervioso central suele ocurrir en lesiones grandes (> 10 cm) 3 . Además, si es factible, se debe realizar el estudio de la placenta en busca de bandas amnióticas, malformaciones arteriovenosas e infartos.…”
Section: Comentariosunclassified
“…2). En grandes lesiones asociadas a defectos óseos, se recomienda la reconstrucción quirúrgica con cierre definitivo con colgajos locales, expansiones tisulares y craneoplastia [3][4][5] .…”
Section: Comentariosunclassified