Arthropathie de l’épaule et syringomyélie

Sharma

Journal of Clinical Imaging Science

et al. 2011

Neuropathic arthropathy of the shoulder is reported in only 5% of cases. Here, we report a rare case of neuropathic arthropathy of the shoulder, secondary to Chiari malformation Type I with associated syringomyelia, that remained undetected for four years. A 38-year-old female presented to our Department with a swelling over the right shoulder that had persisted for four years. X-ray of the joint showed destruction of the head of the right humerus, with typical blunt amputated appearance of the bone and increased joint space. Magnetic resonance imaging showed destruction and lateral dislocation of the head of the humerus. Large amount of fluid collection was seen in and around the right shoulder joint. Neuropathic osteoarthropathy can be defined as bone and joint changes that occurs secondary to loss of sensation. In our case, neuropathic shoulder joint was secondary to syringomyelia associated with Chiari I malformation.

Section: Discussionmentioning

confidence: 99%

“…Neuropathic arthropathy of the shoulder is reported in only 5% of cases. [ 1 ] Here we report a rare case of neuropathic arthropathy of shoulder, secondary to Arnold-Chiari Type I malformation with associated syringomyelia, that was undetected for four years.…”

Section: Introductionmentioning

confidence: 99%

Imaging Findings in Chiari I Malformation with Syringomyelia in a Case of Charcot Shoulder

Sharma

Journal of Clinical Imaging Science

et al. 2011

“…The joints of the upper limb are much less often affected by the process of NA ( 3 ). The shoulder is the most frequent which accounts for only 5% of all Charcot joint locations ( 4 ). Syringomyelia (SM) is a rare and slowly progressive disease characterised by the formation of a fluid-filled cavity called a syrinx, which destroys the spinal cord and causes typical neurological symptoms ( Fig.…”

Section: Introductionmentioning

confidence: 99%

Shoulder arthropathy secondary to syringomyelia: systematic review

Wawrzyniak

Lubiatowski

2023

EFORT Open Reviews

Purpose: The purpose of this study was to collect and evaluate clinical and radiological evidence on shoulder neuroarthropathy (NA) in syringomyelia (SM) that may support the management and treatment of patients with this condition. Materials and methods: This systematic review is based on the analysis of reports available in PubMed, Embase, Cochrane Database of Systematic Reviews and Cochrane Central Register of Controlled Trials using the following keywords: syringomyelia, neuroarthropathy, Charcot joint and shoulder degeneration. Thirty-nine publications were found presenting case reports or case series meeting our criteria. Pooled data included a group of 65 patients and 71 shoulders with NA secondary to SM. Results: The most commonly reported symptoms were range of motion (ROM) limitation, weakness, swelling, pain and dissociated sensory loss. NA is usually monolateral and concerns only the shoulder. The average active shoulder ROM was flexion −59.2° (s.d. 37.9), internal rotation −29.8° (s.d. 22.6) and external rotation −21.1° (s.d. 23.6). Most of the patients (75%) presented with complete or nearly complete proximal humerus degeneration, while the degree of glenoid preservation varied. Fifty-two neuroarthropathic shoulders were treated conservatively with physiotherapy, anti-inflammatory medication and splinting. Eighteen patients were treated by surgical intervention. Conclusion: Shoulder NA due to SM is a devastating and progressive condition, and its course is often unpredictable. Patients with unexplained shoulder degeneration should be evaluated for SM, especially if there are additional neurological symptoms. Conservative treatment usually reduces shoulder pain without improving ROM. For select patients, shoulder arthroplasty may be a better option for restoring function.

VITTALLE, ISSN 1413-3563, Rio Grande, Brasil

“…As causas mais frequentes de siringomielia são: malformação de Arnold-Chiari tipo I, hidrocefalia comunicante, traumas, tumores medulares, medula presa e sua forma idiopática (4). Do total de casos de NA, 5-6% são representados pelo comprometimento do ombro (5,6). Já entre os pacientes com siringomielia 25% desenvolvem NA (7).…”

Section: Introductionunclassified

Neuroartropatia de Charcot secundária à siringomielia com acometimento isolado de ombro: relato de caso

Silva

Campos

Testa

et al. 2020

A neuroartropatia de Charcot do ombro é uma doença degenerativa crônica causada pela perda da sensibilidade articular por diferentes etiologias. Quando ocorre secundariamente a siringomielia, encontramos poucos casos descritos na literatura científica. O diagnóstico precoce é de grande valor, uma vez que o quadro clínico se apresenta de forma inespecífica e pode levar a destruição irreversível da articulação. Com o objetivo de demonstrar a excepcionalidade da doença, alertando a comunidade médica sobre a raridade da enfermidade e o diagnóstico diferencial dentre as demais artropatias degenerativas, descrevemos o caso de um paciente do sexo masculino de 56 anos com neuroartropatia isolada no ombro esquerdo secundária a siringomielia, concluindo que o diagnóstico diferencial é crucial para correta conduta terapêutica.