Ascending aortic aneurysm and diaphragmatic hernia in a case of Marfan syndrome

Kothari, Jignesh; Hinduja, Manish; Baria, Kinnaresh; Pandya, Himani

doi:10.1177/0218492317693694

Cited by 5 publications

(2 citation statements)

References 4 publications

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“…Where Morgagni hernias are repaired in isolation, there is an increasing tendency for laparoscopic repair, although laparotomy accounts for 30% of repairs and thoracotomy for 49% [2]. In patients with concurrent cardiac disease requiring intervention, some surgeons advocate delayed repair of the hernia after cardiac surgery, although combined procedures have been performed with satisfactory outcomes [3].…”

Section: Discussionmentioning

confidence: 99%

Approach to a large rare diaphragmatic hernia in a patient undergoing cardiac surgery

Brookes

Munasinghe

Croagh

et al. 2019

Journal of Surgical Case Reports

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Hernia of Morgagni is an unusual congenital defect of the sternal portion of the diaphragm. Its concurrence with cardiac surgical pathology is rarely described in the literature. Notwithstanding, huge hernia of Morgagni have been noted to cause serious peri-operative impediment and complications. We report the case of a 50-year-old gentleman with a massive Morgagni hernia that threatened strangulation during cardiopulmonary bypass. We describe the combined surgical approach undertaken to repair this hernia, with an accompanying review of the literature relating to misadventure and management of similar large hernia coinciding with cardiac surgery.

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Section: Discussionmentioning

confidence: 99%

Approach to a large rare diaphragmatic hernia in a patient undergoing cardiac surgery

Brookes

Munasinghe

Croagh

et al. 2019

Journal of Surgical Case Reports

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“…More recently was described the simultaneous surgical repair of an ascending aortic aneurysm and a type IV hiatal hernia in a 35-year-old man with Marfan syndrome [30].…”

Section: Anatomical/structural Complicationsmentioning

confidence: 99%

Gastrointestinal Manifestations of Marfan Syndrome

Inayet¹,

Hayat²,

Poullis³

et al. 2017

Preprint

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Symptoms attributed to the gastrointestinal manifestations of multisystem disorders play an important role in the long-term management of these conditions. Gastrointestinal complications of a variety of connective tissue disorders have been studied and there is an increased interest in the incidence and prevalence of these symptoms. Descriptions of the occurrence of gastrointestinal complications in Marfan syndrome have appeared infrequently in the medical literature. In this review article we focus on both structural and functional gastrointestinal pathology that may occur in patients with Marfan syndrome.

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Rare complication of a type IV paraoesophageal hiatal hernia in a Marfan syndrome patient

Hou

Dhanda²,

2021

BMJ Case Rep

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A 77-year-old female patient with Marfan syndrome presented with a 1-week history of worsening malaise and poor appetite. This was associated with a dramatic unintentional loss of weight as well as shortness of breath worsened by exertion. She has significant medical histories of a hiatal hernia and chronic type B aortic dissection. CT scan of the chest was able to confirm a type IV paraoesophageal hiatal hernia compressing on the lower lobe of her left lung without any progression of her aortic dissection. As surgical intervention was contraindicated in light of her advanced age and comorbidities, she was managed conservatively with a clinically satisfied outcome in the short term. Her long-term prognosis, however, is still poor with a high mortality of 1 and 5 years.

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Ascending aortic aneurysm and diaphragmatic hernia in a case of Marfan syndrome

Cited by 5 publications

References 4 publications

Approach to a large rare diaphragmatic hernia in a patient undergoing cardiac surgery

Approach to a large rare diaphragmatic hernia in a patient undergoing cardiac surgery

Gastrointestinal Manifestations of Marfan Syndrome

Rare complication of a type IV paraoesophageal hiatal hernia in a Marfan syndrome patient

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