Associated rare anomalies in prune belly syndrome: A case report

Megacystis Microcolon Intestinal Hypoperistalsis Syndrome: Case Reports and Discussion of the Literature

“…A few MMIHS cases described a thinning of the longitudinal muscle with marked reduction in α-smooth muscle actin in the smooth muscle layer of the bowel and bladder and a proliferation of connective tissue [27]. Histological studies in some PBS cases have also reported an abundance of fibrous tissue and sparsely placed smooth muscle throughout the urinary tract [28]. PBS is characterized by a triad of deficient or absent abdominal wall musculature, hypotonia-ectasia of the urinary system and cryptorchidism [26].…”

Prune belly syndrome: Approaches to its diagnosis and management

“…More than 95% of affected individuals are males (1,3). In fact, fewer than 30 cases of PBS in girls have been reported in the literature (5,6).…”

Prune Belly Syndrome in under Developed Countries: What Perspective in Management

“…Thus it may be lower urinary tract malformations with posterior urethral valves associated with impaired quality of the detrusor and the terminal portion of the urethra. Upper urinary tract malformations are resuming in vesico-ureteral reflux [1][2][3][4]. Urinary stasis cause repeated infections.…”

“…In addition to urinary tract malformations, respiratory system disorders are another entity complicating prune belly syndrome management [3,4]. In this disadvantaged environment endoscopic resection is impossible because of lack of resources.…”

“…Regarding the achievement of the upper urinary tract in front of repeated infections and almost inevitable progression to kidney failure renal transplantation can be the perfect solution [3,4]. Some authors recommend an ureterovesical reimplantation associated with a bladder volume reduction surgery [1].…”