Atypical Polysplenia Only With Absence of the Hepatic Segment of Inferiorvena Cava in a Middle‐aged

Abstract

An autopsy case of polysplenia with absence of the hepatic segment of the inferior vena cava in a 53‐year‐old female is reported. The venous blood from the lower parts of the body was drained through the azygos vein and the superior vena cava into the right atrium. Other than acquired pathological change, the heart was found to be normal. Except for the partial absence of the inferior vena cava, isomerism of asymmetric organs, and heterotaxia of abdominal organs, characteristic of typical polysplenia, were not present. This case of atypical polysplenia suggests the presence of a transitional form in the complex.

Polysplenia syndrome with preduodenal portal vein detected in adults

“…When the incisures fail to fuse, they create two or more spleens [8] . The blood flow of an embryo makes a transition from symmetric to asymmetric around the 25th d to determine the visceral sidedness, and it has been suggested that this is when cono-truncal anomalies and anomalies of atrioventricular canal occur [9] . At the same time, PDPV also develop.…”

Anomalies of Abdominal Organs in Polysplenia Syndrome: Multidetector Computed Tomography Findings

“…This determines the visceral sidedness. Anomalies of conotruncus and the atrioventricular canal occur at this time (19).…”