Autoimmune Pancreatitis Associated with Various Extrapancreatic Lesions during a Long-term Clinical Course Successfully Treated with Azathioprine and Corticosteroid Maintenance Therapy

Abstract

Abstract

Proposal for diagnostic criteria for IgG4-related kidney disease

“…IgG4-RKD is a new clinical entity in the field of nephrology, unrecognized before 2004, when the notion gradually emerged of it being an extrapancreatic manifestation of AIP [2][3][4][5][6][7][8][9][10][11][20][21][22][23][24][25]. This disease has many features helping to distinguish it from other types of TIN radiographically [26][27][28][29][30] and pathologically [11,21], and early detection provides the best chance for preservation of renal function because of its good responsiveness to corticosteroid therapy [2][3][4][5][6][7][8][9][10][11].…”

Characteristic tubulointerstitial nephritis in IgG4-related disease

“…Because steroid therapy has been found to be effective in AIP [1,4,23,24], a proper diagnosis of IgG4-related TIN is very important so that steps can be taken to halt disease progression. Several case reports have described the histologic features of IgG4-related TIN.…”

IgG4-Related Tubulointerstitial Nephritis and Lymphadenopathy after Therapy for Malignant Lymphoma

“…Recently, cases of combined IgG4-related disease and microvasculitis, including HSP/HSPN, have been reported (20,21). HSP of the present case was diagnosed histologically.…”